Cholangiocarcinoma accompanied by desmoid-type fibromatosis

作     者：Nan Xu,Zhe-Yu Chen,Lu-Nan Yan,Jia-Ying Yang,Wen-Tao Wang and Shu-Guang JingDepartment of Liver and Vascular Surgeryand Department of Hepato-biliary-pancreatic Surgery,West China Hospital,Sichuan University, Chengdu 610041,China 

作者机构：Department of Liver and Vascular Surgery West China Hospital Sichuan University Chengdu 610041 China Department of Hepato-biliary-pancreatic Surgery West China Hospital Sichuan University Chengdu 610041 China 

出 版 物：《Hepatobiliary & Pancreatic Diseases International》 (国际肝胆胰疾病杂志（英文版）)

年 卷 期：2011年第10卷第2期

页      面：214-217页

核心收录：

学科分类：1002[医学-临床医学] 100214[医学-肿瘤学] 10[医学] 

主　　题：cholangiocarcinoma desmoid-type fibromatosis diagnosis pancreaticoduodenectomy pathology 

摘      要：BACKGROUND:Cholangiocarcinoma complicated by intraabdominal desmoid-type fibromatosis(DTF)is uncommon. There are no reports on patients with this type of fibromatosis, in which the pre-operative treatment(including diagnosis), surgical approach,post-operative pathologic reports,and prognosis are discussed. METHOD:The clinicopathological features of a 49-year-old man were retrospectively analyzed. RESULTS:Cholangiocarcinoma located in the inferior segment of the bile duct was considered pre-operatively on the basis of clinical *** the time of pancreaticoduodenectomy,the mesojejunum was stiff without nodules or a mass at a distance of approximately 80 cm from the ligament of *** excision of the entire lesion of the intestinal mesenteric contracture and its subsidiary was ***-operative pathologic findings confirmed an adenocarcinoma located at the extremity of the common bile duct and infiltrating the full thickness of the common bile duct as well as the deep muscular layer of the *** contracted jejunal mesentery was shown to have *** patient was alive with no evidence of recurrence after a follow-up of 6 months. CONCLUSIONS:The patient had a rare hereditary disease with intra-abdominal DTF,which manifests the characteristics of an aggressive growth pattern and a high rate of local recurrence; conservative therapy is *** excision of the fibromatous lesion during pancreaticoduodenectomy may maximally decrease the risk of local recurrence.