Isolated arterioportal fistula presenting with variceal hemorrhage

作     者：Anupama Nookala Behnam Saberi Ramon Ter-Oganesyan Gary Kanel Phillip Duong Takeshi Saito 

作者机构：Division of Gastroenterology and Liver Diseases Department of Medicine University of Southern California Los Angeles Department of Radiology University of Southern California Department of Pathology University of Southern California 

出 版 物：《World Journal of Gastroenterology》 (世界胃肠病学杂志（英文版）)

年 卷 期：2013年第19卷第17期

页      面：2714-2717页

核心收录：

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：Arterioportal fistula Presinusoidal portal hypertension Hepatic vein pressure gradient Hepatic artery embolization 

摘      要：We report a case of life-threatening hematemesis due to portal hypertension caused by an isolated arterioportal fistula (APF). Intrahepatic APFs are extremely rare and are a cause of presinusoidal portal hypertension. Etiologies for APFs are comprised of precipitating trauma, malignancy, and hereditary hemorrhagic telangiectasia, but these were not the case in our patient. Idiopathic APFs are usually due to congenital vascular abnormalities and thus usually present in the pediatric setting. This is one of the first cases of adult-onset isolated APF who presented with portal hypertension and was successfully managed through endoscopic hemostasis and subsequent interventional radiological embolization.