Esophageal liposarcoma:Well-differentiated rhabdomyomatous type

作     者：Hisham M Valiuddin Arianna Barbetta Benedetto Mungo Elizabeth A Montgomery Daniela Molena 

作者机构：Lake Erie College of Osteopathic Medicine Bradenton Thoracic Surgery ServiceDepartment of SurgeryMemorial Sloan Kettering Cancer Center Division of Thoracic SurgeryDepartment of SurgeryJohn Hopkins Hospital Division of Gastrointestinal and Liver PathologyDepartment of PathologyJohn Hopkins Hospital 

出 版 物：《World Journal of Gastrointestinal Oncology》 (世界胃肠肿瘤学杂志（英文版）（电子版）)

年 卷 期：2016年第8卷第12期

页      面：835-839页

核心收录：

学科分类：1002[医学-临床医学] 100214[医学-肿瘤学] 10[医学] 

主　　题：Esophageal cancer Esophageal surgery Endoscopy/endoscopic procedures Pathology esophagus Liposarcoma Mesenchymal tumor 

摘      要：Rhabdomyomatous well-differentiated esophageal liposarcomas are extremely rare. As of August 2016, only one other such case has been reported in the English-language medical literature. Liposarcomas in general are one of the most common soft tissue neoplasms in adults, but the incidence of primary esophageal liposarcomas is exceptionally low. There have been only 42 reported cases of primary liposarcoma of the esophagus worldwide thus far. These malignancies are harbored within giant fibrovascular polyps, which slowly grow within the esophageal lumen causing obstructing symptoms. We hereby present the case of a 68-year-old male patient who came in with a 2-mo history of worsening intermittent dysphagia, persistent cough, and postprandial retrosternal pain. After an esophagogastroduodenoscopy, a computed tomographic scan, and a diagnostic endoscopy, complete endoscopic resection was performed of the 13 cm × 6 cm × 2.6 cm fibrovascular polyp. A literature review was done and results are presented herein.