Vestibular rehabilitation in cerebellar ataxia with neuropathy and vestibular areflexia syndrome(CANVAS)-A case report

作     者：R.G.Harrell A.R.Cassidy B.N.Klatt P.Hovareshti S.L.Whitney R.G.Harrell;A.R.Cassidy;B.N.Klatt;P.Hovareshti;S.L.Whitney

作者机构：School of Health and Rehabilitation SciencesDepartment of Physical TherapyUniversity of PittsburghPittsburghPA15219USA Rehabilitation InstituteUniversity of Pittsburgh Medical CenterPittsburghPA15219USA BlueHaloIntelligent AutomationRockvilleMD20855USA Department of OtolaryngologyUniversity of Pittsburgh Medical SchoolPittsburghPA15219USA The University of PittsburghDepartment of Physical Therapy100 Technology Dr.Pittsburgh PA 15219 

出 版 物：《中华耳科学杂志:英文版》 (Journal Of Otology)

年 卷 期：2023年第18卷第4期

页      面：199-207页

核心收录：

学科分类：1002[医学-临床医学] 100213[医学-耳鼻咽喉科学] 10[医学] 

主　　题：vestibular neuropathy meaningful 

摘      要：Background and purpose:Cerebellar ataxia,neuropathy,and vestibular areflexia syndrome(CANVAS)is a neurodegenerative disease of the *** disease progression is slow,with up to 25%of people diagnosed needing to use a wheelchair after 15 years from *** symptoms arise from centrally-mediated ocular movement degradation and the reduced vestibular-ocular reflex functioning *** date,no report has shown an improvement in VOR gain or gait outcome measures in someone with CANVAS after a course of vestibular physical *** description:A 65-year-old male,Patient X,first noticed symptoms in his fourth decade of life and was diagnosed with(CANVAS)in his seventh *** X reported numbness and tingling in his hands and feet,decreased ability to perform daily activities,and several ***:Patient X completed a four-month course of vestibular physical therapy,including vestibular ocular reflex exercises,balance training,gait training,and the VestAid application for eye gaze compliance *** Vestaid application uses eyes and facial recognition software to record the percentage of time that the patient kept their eyes on the ***:After vestibular therapy,Patient X had a clinically meaningful improvement in gait speed:from 1.02 m/s to 1.13 m/s and in the Functional Gait Assessment from 20/30 to 27/*** X s eye gaze compliance improved from a median of 43%(range 25e68%)to a median of 67%(58e83%).Discussion:This case study demonstrates that vestibular rehabilitation improved eye gaze compliance and functional outcomes in a person living with CANVAS.