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neurocutaneous melanosis with an intracranial cystic-solid meningeal melanoma in an adult:A case report and review of literature

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World Journal of Clinical Cases 2022年第15期10卷 5025-5035页

作者： Bo-Chuan Liu Yu-Bo Wang Zhuang Liu Yan Jiao Xian-Feng Zhang Department of Neurosurgery The Second Affiliated Hospital of Xi'an Medical UniversityXi'an 710038Shaanxi ProvinceChina Department of Neurosurgery First Hospital of Jilin UniversityChangchun 130021Jilin ProvinceChina Department of Neurosurgery Dongfeng County HospitalLiaoyuan 136300Jilin ProvinceChina Department of Hepatobiliary and Pancreatic Surgery First Hospital of Jilin UniversityChangchun 130021Jilin ProvinceChina

BACKGROUND neurocutaneous melanosis(NCM)is a rare congenital,nonhereditary neurocutaneous syndrome that mainly occurs in children;adult NCM is very *** to its rarity,the clinical features and treatment strategies for NCM remain *** purpose of this study was to explore the clinical features,diagnosis,treatment and prognosis of NCM in *** intracranial meningeal melanomas are solid masses,and cystic-solid malignant melanomas are very *** to the lack of data,the cause of cystic changes and the effect on prognosis are *** SUMMARY A 41-year-old woman was admitted to the hospital with intermittent headache for 1 *** resonance imaging(MRI)showed a 4.7 cm×3.6 cm cystic-solid mass in the left temporal lobe with peritumoral *** entire mass was removed,and postoperative pathology indicated malignant *** MRI is the first-choice imaging approach for diagnosing central nervous system diseases in NCM patients,although cerebrospinal fluid may also be *** present,there is no optimal treatment plan;gross total resection combined with BRAF inhibitors and MEK inhibitors might be the most beneficial treatment.

关键词： neurocutaneous melanosis Meningeal melanoma Central nervous system disease Adult Cystic-solid tumor Case report

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neurocutaneous melanosis with intraspinal malignant melanoma in adults—an extremely rare clinical entity: A case report with review of literature

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Translational Neuroscience and Clinics 2016年第4期2卷 236-240页

作者： Dongkang Liu Yujun Wei James Wang Guihuai Wang Medical Center Tsinghua University Department of Neurosurgery Beijing Tsinghua Changgung Hospital Medical Center Tsinghua University

Objectives: neurocutaneous melanosis(NCM) in adult patients was rare, and few cases had been reported. In this report, we summarized the features of NCM in adult patients for providing useful information about this rare clinical entity. Methods: In this report, we present a case of a 41-year-old woman, who was eventually diagnosed with NCM with intraspinal malignant melanoma. The clinical features,treatments, and prognosis of cases of NCM in adults were thoroughly reviewed and discussed. Results: A 41-year-old woman was eventually diagnosed with NCM with intraspinal malignant melanoma. The post-operative course was uneventful and her symptoms significantly improved(VAS: 3 points). However, she developed symptoms of intracranial hypertension and deteriorated rapidly after 11 months of operation, and died 1 month later. To date, only 15 cases of NCM in adults have been reported in the English literature. Analyses showed that the average age was 33.8 years(range19–65 years), and 11 patients(68.8%) were between 20 and 40 years. A slight male predominance(M:F/11:5) was found. For the 12 cases which detailed follow-up information was available, 9 patients(75%) died, with a survival time ranging from 1 day to 29 months post-operation. Death occurred within the first month of operation in 6 cases(46. 2%). The median survival time was 3 months. Conclusions: We presented a rare case of NCM with intraspinal malignant melanoma in an adult patient. Although rare, this clinical entity causes significant mortality and has poor prognosis.

关键词： neurocutaneous melanosis spine melanoma adult

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A Case of Coexistence of Aplasia Cutis Congenita and Giant Congenital Melanocytic Nevus:Coexistence of Two Rare Skin Diseases

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Chinese Journal of Plastic and Reconstructive Surgery 2020年第2期2卷 107-108,119页

作者： Ping CHEN Liansheng ZHONG Department of Dermatology XuZhou Children’s HospitalXuZhouChina. Department of Dermatology Children’s hospital of Fudan University Xiamen BranchXiamenChina.

Aplasia cutis congenita(ACC)is a rare disease that is characterized by complete or partial absence of skin at birth,either in a localized or widespread *** nevi refers to tumor-like malformations of the skin or mucous membrane caused by benign proliferation of *** is classified as a giant congenital melanocytic nevus(GCMN)when the diameter of the largest nevus exceeds 20 *** co-occurrence of ACC and GCMN is extremely rare,to the best of our *** report a case of coexistence of ACC and GCMN of infancy in a 2-month-old male *** lesions consisted of a large hyperpigmented plaque occupying most of the trunk and pelvic region,and smaller hyperpigmented plaques on the trunk,head,and ***,there were large,sharply marginated,triangular,depressed atrophic plaques covered by thin,translucent,glistening epithelial membranes in the center of the GCMN on the *** presumptive diagnosis was coexistence of GCMN and *** could be a manifestation of SCALP syndrome,a rare neuro-cutaneous condition characterized by the presence of Sebaceous nevus,Central nervous system(CNS)malformations,Aplasia cutis congenita,Limbal dermoid and Pigmented(giant melanocytic)nevus.

关键词： Aplasia cutis congenita giant congenital melanocytic nevus neurocutaneous melanosis melanoma

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