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World Journal of Clinical Cases 2021年第3期9卷 623-631页

作者： Lan-Xiao Cao Ying Liu zhao-jun song Bao-Rong Zhang Wen-Ying Long Guo-Hua zhao Department of Neurology The Fourth Affiliated HospitalZhejiang University School of MedicineYiwu 322000Zhejiang ProvinceChina Central Laboratory The Fourth Affiliated HospitalZhejiang University School of MedicineYiwu 322000Zhejiang ProvinceChina Department of Neurology The Second Affiliated HospitalZhejiang University School of MedicineHangzhou 310009Zhejiang ProvinceChina

BACKGROUND Type 1 sialidosis,also known as cherry-red spot-myoclonus syndrome,is a rare autosomal recessive lysosomal storage disorder presenting in the second decade of *** most common symptoms are myoclonus,ataxia and *** is rarely encountered in the Chinese *** SUMMARY A 22-year-old male presented with complaints of progressive myoclonus,ataxia and slurred speech,without visual symptoms;the presenting symptoms began at the age of *** exome sequencing revealed two pathogenic heterozygous missense variants[c.239C>T(p.P80L)and c.544A>G(p.S182G)in the neuraminidase 1(NEU1)gene],both of which have been identified previously in Asian patients with type 1 *** three patients identified in China's Mainland come from three unrelated families,but all three show the NEU1 mutations p.S182G and p.P80L pathogenic *** sialidase activity through chaperones is a promising therapeutic target in *** Through retrospective analysis and summarizing the clinical and genetic characteristics of type 1 sialidosis,we hope to raise awareness of lysosomal storage disorders among clinicians and minimize the delay in diagnosis.

关键词： Sialidosis Myoclonus Ataxia Neuraminidase 1 Case report Mucolipidoses

Two-stent strategy for renal artery stenosis with bifurcation lesion

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Journal of Zhejiang University-Science B(Biomedicine & Biotechnology) 2010年第8期11卷 561-567页

作者： Hong-bing YAN Bin ZHENG Zheng WU Jian WANG Han-jun zhao Li song Yun-peng CHI Department of Cardiology Beijing Anzhen Hospital Capital Medical University Beijing 100029 China

Renal artery stenosis(RAS) with a bifurcation lesion is a challenge for interventional *** aim of this study is to summarize our experience in RAS with a bifurcation *** patients with RAS involving bifurcation lesion are *** cases 1 to 3,a single-stent strategy was first ***,these three patients were converted to a two-stent strategy for bailout stent implantation in the side *** cases 4 and 5,a simultaneous kissing stent technique was *** showed that the reference vascular diameter of the main branch was much larger than those of the side *** obvious residual stenosis existed in cases 1 to 3 after stent implantation,no obvious residual stenosis was seen in cases 4 and *** artery duplex sonography was performed in cases 1 through 5 at 6,7,7,8,and 6 months,respectively,after the *** evidence of restenosis or occlusion was *** conclusion,stent implantation with the simultaneous kissing stent technique may result in more simple and more satisfactory immediate angiographic results.

关键词： Peripheral atherosclerotic artery disease Angioplasty Stents Renal artery stenosis

Pacific oyster(Crassostrea gigas)shell growth duration in a year in Bohai Bay and implication for its carbon sink potential

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China Geology 2024年第4期7卷 653-660页

作者： Wen-yu Wang Chang-fu Fan zhao-jun song Hong Wang Fu Wang Qingdao Geotechnical Investigation and Surveying Research Institute Qingdao 266033China MRL Key laboratory of Metallogeny and Mineral Assessment Institute of Mineral ResourcesChinese Academy of Geological SciencesBeijing 100037China College of Earth Science and Engineering Shandong University of Science and TechnologyQingdao 266590China Tianjin Centre China Geological SurveyTianjin 300170China

Oyster is a bivalve mollusk widely distributed in estuarine and shallow sea *** growth and burial process is a carbon sequestration and storage *** shell may stop growing due to suffer from freeze shock during the winter season within a temperate climate,therefore,in order to study the carbon sequestration capacity of oysters we need to know the water temperature at which the shell suffer from winter freeze *** study examinesδ^(18)O profiles across consecutive micro-growth layers found in three modern Pacific oyster shells from the northwest coast of Bohai Bay.A total of 165 oxygen isotope values from sequential samples of their left shells showed periodically varying values,and the variation fluctuation of oxygen isotope values was 4.97‰on *** to the variation range of the oxygen isotope value of the shell,combined with the sea surface temperature and the sea surface salinity data of the water in which the oysters grew,the water temperature that suffer from winter freeze shock and stops or retards the growth of Pacific oysters in Bohai Bay is about 8.3℃,and the corresponding period is from December to March of the following *** calcification time of oysters within one year is nearly a month longer than previously thought,therefore,its carbon sink potential is also improved.

关键词： Crassostrea gigas Winter freeze shock Oxygen isotope Bohai Bay Carbon sequestration and storage Environmental geological survey

Relaxation of Chain Extension of Amorphous PET Fiber Above the Glass Transition Temperature

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Chinese Chemical Letters 2000年第10期11卷 925-928页

作者： Xin LINGHU, jun zhao, Rui song, Qing Rong FAN (Polymer Physics Laboratory, Center of Molecular Science, Institute of Chemistry, Chinese Academy of Sciences, Beijing, 100080) Polymer Physics Laboratory Center of Molecular Science Institute of Chemistry Chinese Academy of Sciences

The recovery of amorphous PET fiber in global chain orientation but nearly random segmental orientation (GOLR) state was studied by the hot shrinkage measurement above the glass transition temperature. The relaxation curves in the form of di-exponential decay were acquired and the change of two special times with the variation of treating temperature and residual recovery ratio ' was discussed.

关键词： GOLR state PET recovery of chain extension hot shrinkage measurement.

Is it necessary to stent renal artery stenosis patients before cardiopulmonary bypass procedures？

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Chinese Medical Journal 2011年第10期124卷 1453-1457页

作者： ZHENG Bin YAN Hong-bing LIU Rui-fang CHENG Shu-juan WANG Jian zhao Han-jun song Li Department of Cardiology Beijing Anzhen Hospital Capital Medical University Beijing 100029 China

Background Acute kidney injury （AKI） is associated with poor prognosis after cardiopulmonary bypass. The aim of this retrospective study was to investigate whether stent implantation before cardiopulmonary bypass has beneficial effect on development of AKI in renal artery stenosis （RAS） *** In this retrospective study, patients with abnormal baseline serum creatinine （SCr, 〉106 μmol/L） were not included. Included patients （n=69） were divided into two groups. Group 1 included 31 RAS patients receiving no stent implantation before cardiopulmonary bypass. Group 2 included 38 RAS patients having received stent implantation just before cardiopulmonary bypass. To assess AKI after cardiopulmonary bypass, serum urea nitrogen, SCr and creatinine clearance were recorded at baseline, at the end of operation, during the first and second postoperative 24 *** Baseline characteristics were similar between groups. Serum urea nitrogen, SCr, creatinine clearance before and after cardiopulmonary bypass were also similar class groups. Incidence of AKI in group 1 was not significantly different from group 2. In group 1, AKI defined by RIFLE between occurred in 7 （22.6%） patients： 5 （16.1%） with RIFLE-R,2 （6.5%） with RIFLE-I, and no patients with RIFLE-F. In group 2, 10 patients （26.3%） had an episode of AKI during hospitalization： 6 （15.8%） had RIFLE-R, 4 （10.5%） had RIFLE-I, and no patients had *** There are no data suggesting that it is necessary to stent RAS patients with normal SCr before cardiopulmonary bypass. However, it cannot be concluded that RAS is not associated with AKI after cardiopulmonary bypass

关键词： renal insufficiency cardiopulmonary bypass peripheral vascular disease renal artery

Resection and repair of large abdominal wall lesions in gynecologic patients

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Chinese Medical Journal 2013年第9期126卷 1673-1677页

作者： LIU Zhu-feng WANG Jin-hui CUI Bing-qian FAN Qing-bo WANG Xiao-jun zhao Ru song Ke-xin Department of Obstetrics and Gynecology Department of Plastic Surgery Peking Union Medical College Hospital Peking Union Medical College Chinese Academy of Medical Science Beijing 100730 China

Background The techniques of resection and repair of large lesions in the abdominal wall are very challenging in the area of gynecology. We explored the techniques of resection and plastic surgical repair of large abdominal wall lesions in gynecologic patients. Methods Twenty-six patients with large lesions in the abdominal wall underwent resection by the gynecologists and repair through abdominal plasty and V-Y plasty with or without fascia patch grafting by the gynecologists or plastic surgeons from March 2003 to October 2010. Results All patients had a history of cesarean section. One patient had an infected sinus tract after cesarean section, one patient had an inflammatory nodule, and the others had lesions of endometriosis, including one cancer. The average largest lesion diameter was （4.79 ± 4.18） cm according to the ultrasonography results. The lesions of all patients were completely resected with pretty abdominal contour. A polypropylene biological mesh was added to the fascia in 20 patients. One patient underwent groin flap repair, and one underwent V-Y advanced skin flap repair on the left of the incision to relieve the suture tension. Conclusions Multi-department cooperation involving the gynecology and plastic surgery departments, and even the general surgery department, is essential for patients with large lesions in the abdominal wall. This cooperative effort enabled surgeons to completely resect large lesions. Abdominal wall plastic surgical repair can ameliorate large wounds of the abdominal wall.

关键词： abdominal wall endometriosis reconstructive surgical procedures abdominoplasty

TRIPLET combined with microwave ablation:A novel treatment for advanced hepatocellular carcinoma

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World Journal of Gastrointestinal Oncology 2025年第1期17卷 10-12页

作者： Fei-Yu zhao Guo-Wei Si Nian-song Qian Department of Thoracic Oncology Respiratory and Critical Care MedicineThe Eighth Medical Center of People’s Liberation Army General HospitalBeijing 100853China Department of Gastroenterology Fourth Medical CentreGeneral Hospital of the People's Liberation ArmyBeijing 100142China Senior Department of Thoracic Oncology Respiratory and Critical Care MedicineThe Eighth Medical Center of People’s Liberation Army General HospitalBeijing 100091China

This editorial comments on a study by Zuo et *** focus is on the efficacy of he-patic arterial infusion chemotherapy combined with camrelizumab and apatinib(the TRIPLET regimen),alongside microwave ablation therapy,in treating advanced hepatocellular carcinoma(HCC).The potential application of this combination therapy for patients with advanced HCC is evaluated.

关键词： Microwave ablation Hepatic arterial infusion chemotherapy Apatinib Camrelizumab Hepatocellular carcinoma

依托环境监测站,打造基层环境保护宣教新平台——以砚山县环境监测站省级环境教育基地创建为例

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环境科学导刊 2018年第A01期37卷 34-37页

作者：赵俊松砚山县环境监测站云南砚山663100

加强环境宣传教育,开展多样性活动激励更多人参与环保,凝聚社会力量,形成污染治理和保护环境的合力是环境保护的一项核心工作。通过在环境监测站创建环境教育基地,能够有效地搭建基层环境保护宣教平台,把基层环境保护工作情况全面生动... 详细信息

加强环境宣传教育,开展多样性活动激励更多人参与环保,凝聚社会力量,形成污染治理和保护环境的合力是环境保护的一项核心工作。通过在环境监测站创建环境教育基地,能够有效地搭建基层环境保护宣教平台,把基层环境保护工作情况全面生动地反映给公众,促进基层环境保护行政主管部门的各项工作顺利开展,推动生态文明建设。

关键词：环境教育基地环境保护宣传教育环境监测站

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听湖水库水质现状调查及保护对策

环境科学导刊 2015年第4期34卷 13-17页

作者：赵俊松砚山县环境监测站云南砚山663100

介绍了砚山县城及听湖水库概况,分析和评价了听湖水库近年来的水质监测数据,通过实地调查,认为听湖水库污染源包括县城污水、径流区村寨污染、小海湾坝污染、水库管理不到位造成的污染、库区养鱼污染、工业污染和内源污染,对水库的环境... 详细信息

介绍了砚山县城及听湖水库概况,分析和评价了听湖水库近年来的水质监测数据,通过实地调查,认为听湖水库污染源包括县城污水、径流区村寨污染、小海湾坝污染、水库管理不到位造成的污染、库区养鱼污染、工业污染和内源污染,对水库的环境保护提出了相应的对策。

关键词：水库现状调查水环境保护污染源调查水库保护对策听湖水库砚山

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基层环境监测站开展环境教育的探讨

环境科学导刊 2016年第A01期35卷 34-36页

作者：赵俊松砚山县环境监测站云南砚山663100

环境监测与环境教育是环境保护的两个重要环节,介绍了在基层环境监测站开展环境教育的方式,这种方式既能使环境监测通过环境教育展现监测成果,又能使环境教育通过环境监测达到模式创新。二者相得益彰,对推动环境保护工作有着积极重要的... 详细信息

环境监测与环境教育是环境保护的两个重要环节,介绍了在基层环境监测站开展环境教育的方式,这种方式既能使环境监测通过环境教育展现监测成果,又能使环境教育通过环境监测达到模式创新。二者相得益彰,对推动环境保护工作有着积极重要的意义。

关键词：环境教育环境监测基层环境监测站