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Clinical and radiographic features of Hutchinson-Gilford progeria syndrome: A case report

World Journal of Clinical Cases 2014年第3期2卷 67-71页

作者： Daniel Berretta Alves Juliana Melo Silva Tatiany Oliveira Menezes rosely santos cavaleiro Fabrício Mesquita Tuji Marcio Ajudarte Lopes Alexandre Augusto Zaia Ricardo Della Coletta Department of Radiology Esperanca Institute of Higher Learning Santarém-Pará 68040-100 Brazil Department of Endodontics Federal University of Pará Belém-Pará 66055-240 Brazil Department of Dentistry for Patients with Special Needs Federal University of Pará Belém-Pará 66055-240 Brazil Department of Oral and Maxillofacial Pathology Federal University of Pará Belém-Pará 66055-240 Brazil Department of Oral Diagnosis School of Dentistry State University of Campinas Piracicaba-Sao Paulo 13083-970 Brazil Department of Restorative Dentistry School of Dentistry State University of Campinas Piracicaba-Sao Paulo 13083-970 Brazil

Hutchinson-Gilford progeria syndrome(HGPS) is a rare dysmorphic syndrome characterized by several features of premature aging with clinical involvement of the skin, bones, and cardiovascular system. HGPS has an estimated incidence of one in four million to one in eight million births. The main clinical features of HGPS include short stature, craniofacial dimorphism, alopecia, bone fragility, and cardiovascular disorders. The most frequent cause of death is myocardial infarction at a mean age of 13 years old. Dental manifestations include delayed development and eruption of teeth, discoloration, crowding and rotation of teeth, and displaced teeth. Cone beam computed tomography images revealed the absence of the sphenoid, frontal, and maxillary sinus, flattening of the condyles and glenoid fossa, and bilateral hypoplasia of the mandibular condyles. The disease is caused by mutations in lamin A/C(LMNA). Here, we present a case report of an 11-year-old boy with classical features of HGPS, which was caused by a de novo germ-line mutation(C1824T, G608G) in exon 11 of the LMNA gene. Some uncommon HGPS-associated features in our patient, such as alterations in the facial sinuses and hypoplasia of the condyles, contributed to the expansion of the phenotypic spectrum of this syndrome from a dentomaxillofacial perspective.

关键词： Cone beam computed tomography LMNA mutation Craniofacial anomalies Temporomandibular joint

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Vehicle Operating, Accident and User Time Costs in Pavement Management Systems： Approach for Portuguese Conditions

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Journal of Civil Engineering and Architecture 2011年第8期5卷 723-731页

作者： Bertha Maria Batista dos santos Luis Guilherme de Picado santos Victor Manuel Pissarra cavaleiro Department of Civil Engineering and Architecture University of Beira Interior Covilha 6200-001 Portugal Department of Civil Engineering and Architecture IST Technical University of Lisbon Lisbon 1049-001 Portugal

This paper presents a description and analysis of the most important models to predict each of the Road User Costs components (Vehicle Operating Costs, Accident Costs and Value of Time) and proposes a model for estimating RUC components suitable for the Portuguese road network. These results are part of a research which aimed to obtain a Road User Cost Model to be used as a tool in road management systems. This model is different from other models by the fact that it includes a simple formulation that allows calibration and calculation of cost parameters, for any year, in a simple and fast way, providing trustworthy results. The required data is already available in Portuguese institutions, allowing periodic revision of cost parameters to insure accuracy.

关键词：时间成本车辆运行路面管理系统葡萄牙事故道路管理系统用户网络模型

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Disordered eating behaviour and eating disorder among adolescents with type 1 diabetes:An integrative review

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World Journal of Meta-Analysis 2022年第5期10卷 244-254页

作者： Maria Conceição santos Oliveira Cunha Francisco Clécio Silva Dutra Laura Martins Mendes cavaleiro Brito Rejane Ferreira Costa Maria Wendiane Gueiros Gaspar Danilo Ferreira Sousa Márcio Flávio Moura deAraújo Maria Veraci Oliveira Queiroz Department of Nursing West Princess CollegeCrateús 63700-190CearáBrazil Department of Nursing Ceara State UniversityFortaleza 60714-903CearáBrazil Department of Health Family Oswaldo Cruz FoundationEusébio 61773-272CearáBrazil Department of Health Science University for the International Integration of Afro-Brazilian LusophonyRedenção 62790-000CearáBrazil Department of Nursing University for the International Integration of Afro-Brazilian LusophonyRedenção 62790-000Brazil

BACKGROUND Type 1 diabetes(DT1)in adolescents brings behavioural changes,altered nutritional habits,and eating *** To identify and analyze the validated instruments that examine the disordered eating behaviour and eating disorders among adolescents with *** An integrative review was accomplished based on the following databases:PubMed,LILACS,CINAHL,Scopus,Web of Science,and Reference Citation Analysis(RCA),including publications in Portuguese,English,or Spanish,without time limit and time *** The main instruments to evaluate disordered eating behaviour were The Diabetes Eating Problem Survey-Revised,The Diabetes Eating Problem Survey,and the eating attitudes test-26,and for eating disorders the main instruments used were The Bulimic Investigation Test of Edinburgh,The Binge Eating Scale,The Child Eating Disorder Examination,The five questions of the(Sick,Control,One,Fat and Food),and The Mind Youth *** instruments showed an effect in evaluating risks regarding nutritional habits or feeding grievances,with outcomes related to weight control,inadequate use of insulin,and glycaemia *** did not identify publication *** Around the world,the most used scale to study the risk of disordered eating behaviour or eating disorder is The Diabetes Eating Problem *** researchers use this scale to identify high scores in adolescents with DT1 and a relationship with poorer glycemic control and psychological problems related to body image.

关键词： Adolescent Type 1 diabetes mellitus Validation studies Nutritional behaviour Eating disorder Review

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Nb-Cr基涂层的微观结构及初期氧化

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中国有色金属学报 2013年第11期23卷 3171-3178页

作者：李月巧李伟洲刘会群易丹青 Albano CAVALEIR0 广西大学材料科学与工程学院南宁530004 中南大学材料科学与工程学院长沙410083 SEG-CEMUC-Department of Mechanical Engineering University of CoimbraRua Luis Reis SantosP-3030 788 CoimbraPortugal

由磁控溅射技术沉积Nb-Cr、Nb-Cr-Al和Al/Nb-Cr 3种涂层,对涂层的微观结构和初期抗氧化性进行研究。结果表明:Nb-Cr涂层呈柱状结构,含Cr2Nb相;Nb-Cr-Al涂层为含非晶组织的柱状结构;Al/Nb-Cr复合涂层的内层保留了Nb-Cr的柱状结构,外层无... 详细信息

由磁控溅射技术沉积Nb-Cr、Nb-Cr-Al和Al/Nb-Cr 3种涂层,对涂层的微观结构和初期抗氧化性进行研究。结果表明:Nb-Cr涂层呈柱状结构,含Cr2Nb相;Nb-Cr-Al涂层为含非晶组织的柱状结构;Al/Nb-Cr复合涂层的内层保留了Nb-Cr的柱状结构,外层无明显特征,涂层包含面心立方(FCC)Al、Cr2Nb和NbAl3等相。在1 200℃氧化60 min后,3种涂层显示出不同的氧化增质方式及生成了性质各异的氧化产物:Nb-Cr涂层呈抛物线方式增质,表面产物为Cr2O3和CrNbO4多孔混合氧化物;Nb-Cr-Al涂层表现出近线性的氧化增质,表面生成以Cr2O3和CrNbO4为外层、Al2O3为内层的复合氧化物层,氧化膜中有裂纹和脱落,涂层主体呈多孔结构;Al/Nb-Cr复合涂层氧化增质轻微,表面膜以Al2O3为主、连续且致密,涂层中保持高Cr含量,Al/Nb-Cr涂层有较强的抗氧化能力。

关键词： Nb-Cr基涂层微观结构高温氧化表面氧化膜

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