检索结果-南通市图书馆

World Journal of Clinical Cases 2021年第13期9卷 3200-3211页

作者： Juan-Juan Zhang Jun-Qi Wang man-qing sun De Xu Yuan Xiao Wen-Li Lu Zhi-Ya Dong Department of Pediatrics Ruijin HospitalShanghai Jiao-Tong UniversitySchool of MedicineShanghai 200025China

BACKGROUND Alström syndrome(AS,OMIM ID 203800)is a rare disease involving multiple organs in children and is mostly reported in non-Chinese *** the Chinese population,there are few reports on the clinical manifestations and pathogenesis of *** is the first report on the association between AS and Graves’*** SUMMARY An 8-year-old Chinese girl was diagnosed with *** years later,Graves’hyperthyroidism developed with progressive liver *** patient’s clinical data were collected;DNA from peripheral blood of the proband,parents and sibling was collected for gene mutation detection using the second-generation sequencing method and gene panel for *** association between the patient’s genotype and clinical phenotype was *** carried the pathogenic compound heterozygous mutation of ALMS1(c.2296_2299del4 and c.11460C>A).These stop-gain mutations likely caused truncation of the ALMS1 *** The manifestation of hyperthyroidism may suggest rapid progression of AS.

关键词： ALMS1 Alström syndrome Stop-gain mutations Protein truncation Graves’hyperthyroidism Case report

Plasmonic tandem heterojunctions enable high-efficiency charge transfer for broad spectrum photocatalytic hydrogen production

维普期刊数据库评论

在线全文

维普期刊数据库

学校读者我要写书评

暂无评论

Journal of Energy Chemistry 2025年第1期100卷 710-720页

作者： Wenxuan Chen Xiu-qing Qiao Guo Hui Bojing sun Dongfang Hou Meidi Wang Xueqian Wu Tao Wu Dong-Sheng Li College of Materials and Chemical Engineering Key Laboratory of Inorganic Nonmetallic Crystalline and Energy Conversion Materials China Three Gorges University Hubei Three Gorges Laboratory College of Chemistry and Materials Science and Guangdong Provincial Key Laboratory of Supramolecular Coordination Chemistry Jinan University

Rational engineering of semiconductor photocatalysts for efficient hydrogen production is of great significance but still challenging,primarily due to the limitations in charge transfer ***,a fascinating plasmonic tandem heterojunction with the hc-CdS/Mo2C@C heterostructure is aimfully prepared for effectively promoting the charge separation kinetics of the CdS photocatalyst via the synergistic strategy of phase junction,Schottky junction,and photothermal *** difference in atomic configuration between cubic-CdS （c-CdS） and hexagonal-CdS （h-CdS） leads to effective charge separation through a typical Ⅱ charge transfer mechanism,and plasmonic Schottky junction further extracts the electrons in the hc-CdS phase junction to realize gradient charge ***,the photothermal effect of Mo2C@C helps to expand the light absorption,accelerate charge transfer kinetics,and reduce the hydrogen evolution energy *** carbon layer provides a fast channel for charge transfer and protects the photocatalyst from *** a result,the optimized hc-CMC photocatalyst exhibits a significantly high photocatalytic H2production activity of 28.63 mmol/g/h and apparent quantum efficiency of 61.8%,surpassing most of the reported *** study provides a feasible strategy to enhance the charge transfer kinetics and photocatalytic activity of CdS by constructing plasmonic tandem heterogeneous junctions.

关键词： Heterojunctions LSPR Photocatalyst Phase junction Schottky junction Photothermal effect

最大限度降低生产成本是电石法生产PVC企业的唯一出路

在线全文

同方期刊数据库

学校读者我要写书评

暂无评论

聚氯乙烯 2002年第4期30卷 17-20页

作者：王满庆孙剑飞牡丹江鑫利化工有限责任公司黑龙江牡丹江157009

分析了影响电石法PVC树脂成本的因素 ,指出电石法生产PVC树脂的企业降低生产成本的出路是降低电石、氯化氢和能源的消耗 ,并详细介绍了降低这三项消耗要采取的相应措施。实施改进措施后可使PVC生产成本降低约 2 1 2元 /t,这样可节约资金... 详细信息

分析了影响电石法PVC树脂成本的因素 ,指出电石法生产PVC树脂的企业降低生产成本的出路是降低电石、氯化氢和能源的消耗 ,并详细介绍了降低这三项消耗要采取的相应措施。实施改进措施后可使PVC生产成本降低约 2 1 2元 /t,这样可节约资金 4 2 4万元 /a(以产能为 2万t/aPVC计 ) 。

关键词：生产成本电石法 PVC企业聚氯乙烯经济效益

在线全文

学校读者我要写书评

暂无评论

环境工艺方法论研究——上天入地法

四川环境 2011年第5期30卷 143-146页

作者：舒曼龙炳清孙彦君刁剑四川师范大学化学与材料学院成都610066

上天入地法是环境工艺技术一般方法的重要组成部分。文章给出了上天入地法的定义,在环境工艺中的应用实例,并探究了其哲学内涵。

关键词：环境工艺方法论上天入地法

Ginkgo Huolinhensis *** the Lower Cretaceous of Huolinhe Coal Field,Inner Mongolia,China

在线全文

学校读者我要写书评

暂无评论

Acta Geologica Sinica(English Edition) 2012年第1期86卷 11-19页

作者： DONG man sun Ge Research Center of Palaeontology and Stratigraphy Jilin UniversityChangchun 130026China Key Lab for Evolution of Past Life and Environment in NEAsia Ministry of EducationChina(Jilin University)Changchun 130026China Palaeontological Institute Shenyang Normal UniversityShenyang 110034China

A new species, Ginkgo huolinhensis sp. nov., with well-preserved cuticle from the Lower Cretaceous, Huolinhe Formation of Huolinhe Coal Field in Inner Mongolia, China, was studied morphologically and anatomically. The main characters of the new species are found in the leaves which are deeply dissected with narrow lobes, trichomes developed on both upper and lower epidermal cells, a media papilla developed on the periclinal walls for each cell in upper cuticle, and no trichomes on the cuticle of the petioles. These characters of G. huolinhensis sp. nov. distinguish from the known species of Ginkgo previously reported. This study of the new species is beneficial for the taxonomic research of fossil Ginkgo, and should be helpful for a better understanding the paleoenvironment of Ginkgo living in northeastern China during the Early Cretaceous.

关键词： new species Ginkgo Early Cretaceous Huolinhe Inner Mongolia

A novel polystyrene-poly(hydroxamic acid)interpenetrating polymer network and its adsorption towards rare earth ions

在线全文

学校读者我要写书评

暂无评论

Journal of Rare Earths 2022年第1期40卷 127-134页

作者： Xiaoyan Cao qing Wang Shuai Wang Ruilin man College of Chemistry and Chemical Engineering Hunan Provincial Key Laboratory of Efficient and Clean Utilization of Manganese ResourcesCentral South UniversityChangsha 410083China School of Chemical and Environmental Engineering Jiangxi Province Engineering Research Center of Ecological Chemical IndustryJiujiang UniversityJiujiang 332005China

A novel polystyrene-poly(hydroxamic acid)interpenetrating network resin(PS-PHA IPNs)was successfully synthesized by suspension polymerization and interpenetrating network *** effects of various experimental parameters,including pH,contact time and initial concentrations of rare earth ions on the adsorption capacity were discussed in *** the condition of pH 4.0(La^(3+)),1.0(Ce^(3+))and 3.0(Y^(3+)),respectively,PS-PHA IPNs can reach equilibrium adsorption in 6 h and get maximum adsorption capacities(1.08,1.43 and 1.36 mmol/g).The adsorption process of PS-PHA IPNs for La(Ⅲ),Ce(Ⅲ)and Y(Ⅲ)ions can be described by liquid membrane diffusion,particle diffusion and chemical *** adsorption process is a spontaneous and endothermic process and can be better simulated by Langmuir adsorption *** studies of SEM-EDS indicate that rare earth ions are adsorbed on the surface of PS-PHA *** transform infrared spectroscopy(FTIR)and X-ray photoelectron spectroscopy(XPS)analysis further prove that rare earth ions are chemisorbed on the surface of PS-PHA *** results reveal that the as-prepared PS-PHA IPNs is a promising adsorbent for adsorption of rare earth ions due to their higher adsorption capacity than other adsorbents.

关键词： Adsorption Interpenetrating polymer networks Synthesis Rare earth ions

Realization of arbitrary two-qubit quantum gates based on chiral Majorana fermions

在线全文

学校读者我要写书评

暂无评论

Chinese Physics B 2021年第4期30卷 43-54页

作者： qing Yan qing-Feng sun International Center for Quantum Materials School of PhysicsPeking UniversityBeijing 100871China CAS Center for Excellence in Topological Quantum Computation University of Chinese Academy of SciencesBeijing 100190China Collaborative Innovation Center of Quantum Matter Beijing 100871China Beijing Academy of Quantum Information Sciences Beijing 100193China

Quantum computers are in hot-spot with the potential to handle more complex problems than classical computers *** the quantum computation requires the universal quantum gate set {T,H,CNOT} so as to perform any unitary transformation with arbitrary *** we first briefly review the Majorana fermions and then propose the realization of arbitrary two-qubit quantum gates based on chiral Majorana *** cells consist of a quantum anomalous Hall insulator surrounded by a topological superconductor with electric gates and quantum-dot structures,which enable the braiding operation and the partial exchange *** defining a qubit by four chiral Majorana fermions,the singlequbit T and H quantum gates are realized via one partial exchange operation and three braiding operations,*** entangled CNOT quantum gate is performed by braiding six chiral Majorana ***,we design a powerful device with which arbitrary two-qubit quantum gates can be realized and take the quantum Fourier transform as an example to show that several quantum operations can be performed with this space-limited ***,our proposal could inspire further utilization of mobile chiral Majorana edge states for faster quantum computation.

关键词： quantum computation T gate CNOT gate braiding chiral Majorana fermions

Selberg＇s Integral for Ramanujan Automorphic Representation

在线全文

学校读者我要写书评

暂无评论

Acta Mathematica Sinica,English Series 2011年第7期27卷 1449-1454页

作者： qing Feng sun Department of Mathematics Shandong University Ji'nan 250100 P. R. China

Let π△ be the automorphic representation of GL（2, QA） associated with Ramanujan modular form A and L（s, π△） the global L-function attached to π△. We study Selberg＇s integral for the automorphic L-function L（s, π△） under GRH. Our results give the information for the number of primes in short intervals attached to Ramanujan automorphic representation.

关键词： Automorphic L-functions Selberg's integral primes in short intervals

敦煌三危山出产多色颜料的矿物学及谱学特征研究

维普期刊数据库评论

在线全文

维普期刊数据库

学校读者我要写书评

暂无评论

光谱学与光谱分析 2025年第1期45卷 152-159页

作者：李林筱谭宇辰先怡衡铁付德孙满利艾昊梁云孙凤西北大学文化遗产学院陕西西安710127 中国国家博物馆北京100006

敦煌三危山火焰沟发现一处古代多色颜料开采遗址,该遗址的发现对研究我国西北地区古代矿物颜料的来源有着一定的学术意义。为判断三危山出产颜料的矿物种属及其谱学特征,本文应用偏光显微镜、X射线衍射、激光拉曼光谱、X射线荧光光谱多... 详细信息

敦煌三危山火焰沟发现一处古代多色颜料开采遗址,该遗址的发现对研究我国西北地区古代矿物颜料的来源有着一定的学术意义。为判断三危山出产颜料的矿物种属及其谱学特征,本文应用偏光显微镜、X射线衍射、激光拉曼光谱、X射线荧光光谱多种光谱分析手段对所出产多色颜料矿物开展科学分析。结果表明,三危山古矿出产矿物颜料属天然矿物,主要化学成分为Fe_(2)O_(3)(平均含量66%)和SiO_(2)等,部分样品呈现富硅铝的特征,且均存在不同程度的烧失;主要物相以赤铁矿、针铁矿为主,少许铁矾类,脉石矿物包括石英、高岭石及少许黏土矿物。同时进一步通过拉曼光谱对矿物颜料的显色物相进行分析,2号亮黄色矿物显色物相和前述主要物相一致,均为铁矾类(黄钾铁矾和黄钠铁矾)。除4号样品外,所有呈红棕色的样品主要显色物相均为α-Fe_(2)O_(3)即赤铁矿,而4号样品显色物相为针铁矿,呈色本应为黄色,但致其呈色变为红棕色是由于和赤铁矿伴生存在,且赤铁矿显色能力远强于针铁矿,故改变了4号样品的呈色。综上,该古矿遗址所出产的红色矿物颜料主要为赤铁矿,黄色矿物颜料为黄钾铁矾和黄钠铁矾。黄钾铁矾作为优良的颜料,在岩画及壁画也多有使用,但在莫高窟目前已研究的壁画上暂未发现使用,三危山古矿实证了铁矾类颜料矿物的存在,该发现在一定程度上拓宽了对西北地区黄色矿物颜料的维度。同时也为后续研究该矿冶遗址出产颜料的流向,提供了基础性的数据支撑。

关键词：敦煌采矿遗址矿物颜料呈色拉曼光谱

Austenite Grain Growth Behavior of X80 Pipeline Steel in Heating Process

在线全文

学校读者我要写书评

暂无评论

Journal of Iron and Steel Research International 2010年第3期17卷 62-66页

作者： DUAN Lin-na WANG Ji-man LIU qing-you sun Xin-jun CAO Jian-chun Faculty of Materials and Metallurgy Engineering Kunming University of Science and Technology Kunming 650093 Yunnan China Institute for Structural Materials Central Iron and Steel Research Institute Beijing 100081 China

在Through changing soaking temperature and soaking time, austenite grain growth behavior of X80 pipeline steel under different heating conditions was studied. Relationships of average grain size to soaking temperature and time were obtained respectively. The results show that the prior austenite grains grow with the increase of soaking temperature and time. When soaking temperature is lower than 1 180 ℃, austenite grain size and growth rate are small; when it higher than 1 200 ℃, austenite grains grow rapidly and abnormal grain growth appears. For soaking at 1 180 ℃, austenite grain growth rate is initially high and then decreases when soaking time exceeds 1 h.

关键词： soaking temperature soaking time grain growth grain size