检索结果-南通市图书馆

a.tosoma. recessive cerebella. a.a.ia.with spa.ticity due to a.ra.e muta.ion in GBa. gene in a.la.ge consa.guineous Sa.di fa.ily

引用

Genes & Disea.es 2021年第1期8卷 110-114页

作者： hussein a.ga.ta.i Ba.er Shira. Ikra. ullah Moha.ma. H.a.-Qa.ta.i a.gha. a.dulra.ma. a.dulka.eem Muha.ma. Imra. Na.eer King a.dula.iz Medica. City King Saud bin Abdulaziz University for Health SciencesJeddahSaudi Arabia King ab.ullah Interna.iona. Medica. Resea.ch Center King Saud bin Abdulaziz University for Health SciencesJeddahSaudi Arabia Sula.ma. Bin ab.ullah a.a.a.-Kha.l Centre for Interdisciplina.y Resea.ch in Ba.ic Sciences International Islamic UniversityIslamabadPakistan Center of Excellence in Genomic Medicine Resea.ch King Abdulaziz UniversityJeddahSaudi Arabia Depa.tment of Medica. La.ora.ory Technology Faculty of Applied Medical SciencesKing Abdulaziz UniversityJeddahSaudi Arabia

The nonlysosoma. glucosylcera.ida.e b2(GBa.)gene encode a. enzyme tha. ca.a.yzes the hydrolysis of glucosylcera.ide to glucose a.d *** in the GBa. gene ha.e been reported to ca.se heredita.y spa.tic pa.a.legia.a.tosoma. recessive cerebella. a.a.ia.with spa.ticity,a.d Ma.inescu-Sjogren-Like *** this study,we report the clinica. fea.ures a.d genetic dia.nosis of a.tosoma. recessive cerebella. a.a.ia.with spa.ticity due to a.ra.e muta.ion in GBa. gene in a.la.ge consa.guineous Sa.di *** included a.la.ge consa.guineous Sa.di fa.ily with a.presumptive clinica. dia.nosis of a.a.ia.a. King a.dula.iz Medica. City in Jedda.,Sa.di *** fa.ily included six a.fected individua.s a.d four una.fected in a.dition to the *** exome sequencing(WES)wa. performed for the proba.dⅣ-5,a.d Sa.ger sequencing wa. used to confirm the va.ia.t in other fa.ily *** study wa. performed using DNa.from the pa.ents a.d siblings of the *** a.a.ysis identified a.homozygous va.ia.t c.2618G>a.p.(a.g873His)in GBa. *** homozygous va.ia.t wa. identified in a.fected members of the fa.ily while the pa.ents a.d the other four siblings were heterozygous ca.riers of the *** sibling wa. not a.a.la.le for genetic *** va.ia.t identified in our pa.ients is cla.sified a. pa.hogenic considering the current evidence of the *** recessive cerebella. a.a.ia.with spa.ticity is a. extremely ra.e genetic disorder with very few ca.es reported in the *** conclude tha. the c.2617G>a.muta.ion in GBa. gene ca.ses the loss of function with a.olishment of the enzyma.ic a.tivity tha. ca.ses the *** report a.ds further evidence to support the pa.hogenicity of this *** pa.ients ha. the cla.sica. clinica. phenotype of cerebella. a.a.ia.a.d spa.ticity consistent with previous reports in the litera.ure.

关键词： a.a.ia.with spa.ticity a.tosoma. recessive GBa. Novel muta.ion Sa.di a.a.ia

来源：

维普期刊数据库评论

在线全文

维普期刊数据库

学校读者我要写书评

暂无评论

Investiga.ing the Releva.ce of a.a.ic Text Cla.sifica.ion Da.a.ets Ba.ed on Supervised Lea.ning

引用

Journa. of Electronic Science a.d Technology 2022年第2期20卷 187-208页

作者： a.ma. hussein a.a.neh the Computer Science Depa.tment American University of MadabaMadaba 2882

Tra.ning a.d testing different models in the field of text cla.sifica.ion ma.nly depend on the pre-cla.sified text document da.a.ets. Recently, seven da.a.ets ha.e emerged for a.a.ic text cla.sifica.ion, including Single-La.el a.a.ic News a.ticles Da.a.et(Sa.a.), Kha.eej, a.a.iya. a.hba.ona. Ka.IMa., Wa.en2004, a.d Kha.eej2004. This study investiga.es which of these da.a.ets ca. provide significa.t tra.ning a.d fa.r eva.ua.ion for text cla.sifica.ion(TC). In this investiga.ion, well-known a.d a.cura.e lea.ning models a.e used, including na.ve Ba.es(NB), ra.dom forest(RF), K-nea.est neighbor(KNN), support vector ma.hines(SVM), a.d logistic regression(LR) models. We present releva.ce a.d time mea.ures of tra.ning the models with these da.a.ets to ena.le a.a.ic la.gua.e resea.chers to select the a.propria.e da.a.et to use ba.ed on a.solid ba.is of compa.ison. The performa.ces of the five lea.ning models a.ross the seven da.a.ets a.e mea.ured a.d compa.ed with the performa.ces of the sa.e models tra.ned on a.well-known English la.gua.e da.a.et. The a.a.ysis of the releva.ce a.d time scores shows tha. tra.ning the SVM model on Kha.eej a.d a.a.iya.obta.ned the most significa.t results in the shortest a.ount of time,with the a.cura.y of 82%.

关键词： shortest ena.le neighbor

来源：

维普期刊数据库

同方期刊数据库评论

在线全文

学校读者我要写书评

暂无评论

Optimiza.ion of the mecha.ica. performa.ce a.d da.a.e fa.lure cha.a.teristics of la.ina.ed composites ba.ed on fiber orienta.ion

引用

Frontiers of Structura. a.d Civil Engineering 2023年第9期17卷 1357-1369页

作者： hussein Da.FI a.wer a.-OBa.DI a.da.a.eer Ta.IQ hussein Ra.Za. Roha. Ra.IEE Mecha.ica. Depa.tment College of EngineeringUniversity of WasitKut 35140Iraq Composites Resea.ch La.ora.ory Faculty of New Sciences and TechnologiesUniversity of TehranTehran 33134Iran

In this study,the effect of fiber a.gle on the tensile loa.-bea.ing performa.ce a.d da.a.e fa.lure cha.a.teristics of gla.s composite la.ina.es wa. investiga.ed experimenta.ly,a.a.ytica.ly,a.d *** gla.s fa.ric in the la.ina.e wa. perfectly a.igned a.ong the loa. direction(i.e.,a. 0°),offset a. a.gles of 30°a.d 45°,or mixed in different directions(i.e.,0°/30°or 0°/45°).The composite la.ina.es were fa.rica.ed using va.uum-a.sisted resin *** influence of fiber orienta.ion a.gle on the mecha.ica. properties a.d stiffness degra.a.ion of the la.ina.es wa. studied via.cyclic tensile strength ***,simula.ions ha.e been conducted using finite element a.a.ysis a.d a.a.ytica. a.proa.hes to eva.ua.e the influence of fiber orienta.ion on the mecha.ica. performa.ce of gla.s *** testing revea.ed tha.,a.though the composite la.ina.es la.d a.ong the 0°direction exhibited the highest stiffness a.d strength,their structura. performa.ce deteriora.ed *** a.so determined tha. increa.ing the fiber offset a.gle(i.e.,30°)could optimize the mecha.ica. properties a.d da.a.e fa.lure cha.a.teristics of gla.s *** results of the numerica. a.d a.a.ytica. a.proa.hes demonstra.ed their a.ility to ca.ture the mecha.ica. beha.ior a.d da.a.e fa.lure modes of composite la.ina.es with different fiber orienta.ions,which ma. be used to prevent the ca.a.trophic fa.lures tha. occur in composite la.ina.es.

关键词： fiber orienta.ion composite la.ina.es stiffness degra.a.ion a.a.ytica. a.proa.hes finite element a.a.ysis

来源：

维普期刊数据库

同方期刊数据库评论

在线全文

学校读者我要写书评

暂无评论

Development of the Supply Cha.n Oriented Qua.ity a.sura.ce System for a.rospa.e Ma.ufa.turing SMEs a.d Its Implementa.ion Perspectives

引用

Chinese Journa. of Mecha.ica. Engineering 2016年第6期29卷 1067-1073页

作者： hussein ab.ullahi CHENG Ka. College of Engineering Design and Physical Sciences Brunel University London

a.rospa.e ma.ufa.turing SMEs a.e continuously fa.ing the cha.lenge on ma.a.ing their supply cha.n a.d complying with the a.rospa.e ma.ufa.turing qua.ity sta.da.d requirement due to their la.k of resources a.d the na.ure of business. In this pa.er, the ERP system ba.ed a.proa.h is presented to qua.ity control a.d a.sura.ce work in light of sea.less integra.ion of in-process production da.a.a.d informa.ion interna.ly a.d therefore ma.a.ing suppliers more effectively a.d efficiently. The a.rospa.e Ma.ufa.turing Qua.ity a.sura.ce Sta.da.d （BS/EN9100） is one of the most recognised a.d essentia. protocols for developing the industry-opera.ed-a.d-driven qua.ity a.sura.ce systems. The resea.ch investiga.es using the ERP ba.ed system a. a. ena.ler to implement BS/EN9100 qua.ity ma.a.ement system a. ma.ufa.turing SMEs a.d the a.socia.ed implementa.ion a.d a.plica.ion perspectives. a. a.plica.ion ca.e study on a.ma.ufa.turing SME is presented by using the Sa. ba.ed implementa.ion, which helps fia.ther eva.ua.e a.d va.ida.e the a.proa.h a.d a.plica.ion system development.

关键词： BS/EN 9100 Qua.ity a.sura.ce a.rospa.e ma.ufa.turing ERP system a.rospa.e qua.ity a.sura.ce Sa. progra.ming

来源：

维普期刊数据库

同方期刊数据库评论

在线全文

学校读者我要写书评

暂无评论

Necessa.y a.d Sufficient Optima.ity Conditions for Rela.ed a.d Strict Control of Forwa.d-Ba.kwa.d Doubly SDEs with Jumps Under Full a.d Pa.tia. Informa.ion

引用

Journa. of Systems Science & Complexity 2020年第6期33卷 1804-1846页

作者： a.-hussein a.dulRa.ma. GHERBa. Boula.hra. Depa.tment of Ma.hema.ics College of ScienceQassim UniversityBuraydah 51452Saudi Arabia La.ora.ory of Ma.hema.ica. a.a.ysis Probability and OptimizationUniversity of Mohamed KhiderBiskrua07000Algeria

This pa.er derives necessa.y a.d sufficient conditions of optima.ity in the form of a.stocha.tic ma.imum principle for rela.ed a.d strict optima. control problems with *** problems a.e governed by multi-dimensiona. forwa.d-ba.kwa.d doubly stocha.tic differentia. equa.ions(FBDSDEs)with Poisson jumps a.d ha. firstly rela.ed controls,which a.e mea.ure-va.ued processes,a.d secondly,a. a. a.plica.ion,the a.thors a.low them to ha.e strict *** FBDSDEs with jumps a.e fully-coupled,the forwa.d a.d ba.kwa.d equa.ions work in different Euclidea. spa.es in genera.,the ba.kwa.d equa.ion is Ma.kovia.,a.d the control problems a.e considered under full informa.ion or pa.tia. informa.ion in terms ofσ-a.gebra. tha. provide such *** formula.ion of these equa.ions a. well a. performa.ce functiona.s a.e given in a.stra.t forms to a.low the possibility to cover most of the a.plica.ions a.a.la.le in the ***,coefficients of such equa.ions a.e a.lowed to depend on control va.ia.les.

关键词： a.joint equa.ions forwa.d-ba.kwa.d doubly stocha.tic differentia. equa.ions ma.imum principle necessa.y conditions Poisson process rela.ed control strict control sufficient conditions

来源：

维普期刊数据库

同方期刊数据库评论

在线全文

学校读者我要写书评

暂无评论

Nea.-zero stiffness a.celerometer with buckling of tuna.le electrotherma. microbea.s

引用

Microsystems & Na.oengineering 2024年第2期10卷 67-81页

作者： hussein hussein Chen Wa.g Rui a.endoeira.Esteves Micha.l Kra.t Hossein Fa.iborzi Depa.tment of Mecha.ica. Engineering MSFEAAmerican University of BeirutBeirut11072020Lebanon King ab.ullah University of Science a.d Technology Thuwal23955-6900Saudi Arabia ESa.-MNS University of Leuven3001LeuvenBelgium

Pre-sha.ed microbea.s,curved or inclined,a.e widely used in MEMS for their interesting stiffness *** mecha.isms a.low a.wide ra.ge of positive a.d nega.ive stiffness tuning in their direction of motion.a.mecha.ism of pre-sha.ed bea.s with opposite curva.ure,connected in a.pa.a.lel configura.ion,ca. be electrotherma.ly tuned to rea.h a.nea.-zero or nega.ive stiffness beha.ior a. the a.-fa.rica.ed *** simple structure helps incorpora.e the tuna.le spring mecha.ism in different designs for a.celerometers,even with different tra.sduction *** sensitivity of the a.celerometer ca. be considera.ly increa.ed or tuned for different a.plica.ions by electrotherma.ly cha.ging the stiffness of the spring *** inclined bea.s a.e implemented in a.ca.a.itive microma.hined *** mea.urements on fa.rica.ed prototypes showed more tha. 55 times ga.n in sensitivity compa.ed to their initia. *** experiments showed promising results in enha.cing the resolution of a.celera.ion sensing a.d the potentia. to rea.h unprecedent performa.ce in microma.hined a.celerometers.

关键词： properties. mecha.ism. stiffness

来源：

维普期刊数据库评论

在线全文

维普期刊数据库

学校读者我要写书评

暂无评论

Imba.a.ced Da.a.Cla.sifica.ion Using SVM Ba.ed on Improved Simula.ed a.nea.ing Fea.uring Synthetic Da.a.Genera.ion a.d Reduction

引用

Computers, Ma.eria.s & Continua 2023年第4期75卷 547-564页

作者： hussein Ibra.im hussein Sa.d a.irul a.wa. Muha.ma. Imra. a.ma. Depa.tment of Computer Techniques Engineering AlSafwa University CollegeKarbala56001Iraq Fa.ulty of Electronic Engineering&Technology Universiti Malaysia PerlisArau02600PerlisMalaysia

Imba.a.ced da.a.cla.sifica.ion is one of the ma.or problems in ma.hine *** imba.a.ced da.a.et typica.ly ha. significa.t differences in the number of da.a.sa.ples between its *** most ca.es,the performa.ce of the ma.hine lea.ning a.gorithm such a. Support Vector Ma.hine(SVM)is a.fected when dea.ing with a. imba.a.ced *** cla.sifica.ion a.cura.y is mostly skewed towa.d the ma.ority cla.s a.d poor results a.e exhibited in the prediction of minority-cla.s *** this pa.er,a.hybrid a.proa.h combining da.a.pre-processing technique a.dSVMa.gorithm ba.ed on improved Simula.ed a.nea.ing(Sa.wa. ***,the da.a.preprocessing technique which prima.ily a.ms a. solving the resa.pling stra.egy of ha.dling imba.a.ced da.a.ets wa. *** this technique,the da.a.were first synthetica.ly genera.ed to equa.ize the number of sa.ples between cla.ses a.d followed by a.reduction step to remove redunda.cy a.d duplica.ed *** is the tra.ning of a.ba.a.ced da.a.et using *** this a.gorithm requires a. itera.ive process to sea.ch for the best pena.ty pa.a.eter during tra.ning,a. improved Sa.a.gorithm wa. proposed for this *** this proposed improvement,a.new a.cepta.ce criterion for the solution to be a.cepted in the Sa.a.gorithm wa. introduced to enha.ce the a.cura.y of the optimiza.ion *** works ba.ed on ten publicly a.a.la.le imba.a.ced da.a.ets ha.e demonstra.ed higher a.cura.y in the cla.sifica.ion ta.ks using the proposed a.proa.h in compa.ison with the conventiona. implementa.ion of *** a. a. a.era.e of 89.65%of a.cura.y for the bina.y cla.s cla.sifica.ion ha. demonstra.ed the good performa.ce of the proposed works.

关键词： Imba.a.ced da.a resa.pling technique da.a.reduction support vector ma.hine simula.ed a.nea.ing

来源：

维普期刊数据库评论

在线全文

维普期刊数据库

学校读者我要写书评

暂无评论

Study on genetic coa.a.ta.ility of wild qua.l popula.ions in China

引用

Science China.Life Sciences) 2006年第2期49卷 172-181页

作者： Ha.Sa. hussein a.ima. Science & Technology College Yangzhou University

Genetic coa.a.ta.ility of wild Ja.a.ese qua.l, wild Common qua.l a.d Domestic qua.l popula.ions in China.wa. studied using 7 microsa.ellite DNa.ma.kers a.d Monte Ca.lo method to test genetic disequilibrium. The molecula. effects of genetic coa.a.ta.ility were a.a.yzed through a.new sta.istica. model of neutra. site. The results showed tha. genetic coa.a.ta.ility domina.ed the genetic disequilibrium of the three qua.l popula.ions, a.d tota.ly 16.67%, 9.66% a.d 10.05% of non-a.lelic combina.ions were in the genetic disequilibrium in wild Ja.a.ese qua.l, wild Common qua.l a.d Do-mestic qua.l popula.ions, respectively. Genetic coa.a.ta.ility existed a. a.most a.l the tested sites. In the molecula. point of view, genetic coa.a.ta.ility pla.s a. importa.t role of keeping lots of poly-morphisms in na.ura. popula.ions. Therefore, it is a.other key fa.tor to the genetic disequilibrium in the popula.ion except for linka.e. The results enrich the conceptions a.d connota.ions of genetic disequilibrium, a.d help us know more a.out genetic coa.a.ta.ility a.d its effects, a.d la. a.founda.tion of eva.ua.ion a.d protection of wild qua.l genetic resources in China.

关键词： microsa.ellite, wild qua.l, genetic coa.a.ta.ility, linka.e, genetic disequilibrium.

来源：

维普期刊数据库

同方期刊数据库评论

在线全文

学校读者我要写书评

暂无评论

Ha.vest a.d Postha.vest Fa.tors a.fecting Bruise Da.a.e of Fresh Fruits

引用

Horticultura. Pla.t Journa. 2020年第1期6卷 1-13页

作者： Za.a.a. hussein Ola.iyi a.a.ole Umezuruike Linus Opa.a Postha.vest Technology Resea.ch La.ora.ory South African Research Chair in Postharvest TechnologyDepartment of Food ScienceFaculty of AgriSciencesStellenbosch UniversityStellenbosch 7602South Africa Postha.vest Technology Resea.ch La.ora.ory South African Research Chair in Postharvest TechnologyDepartment of Horticultural ScienceFaculty of AgriSciencesStellenbosch UniversityStellenbosch 7602South Africa

Fresh fruits a.e susceptible to bruising, a.common type of mecha.ica. da.a.e during ha.vest a.d a. a.l sta.es of postha.vest ha.dling. In quest of developing a.d a.option of stra.egies to reduce bruise da.a.e, it is of utmost importa.ce to understa.d ma.or fa.tors influencing bruise susceptibility of fresh produce a. these sta.es. This review presents a.critica. discussion of fa.tors a.fecting bruising during ha.vest a.d postha.vest ha.dling of fresh fruits. Excessive compression forces during ha.vesting by ha.dpicking or ma.hines, a.d a.series of impa.ts during ha.vesting, tra.sport a.d pa.khouse opera.ions ca. ca.se severe bruise da.a.e. The review ha. further revea.ed tha. bruising is dependent on a.number of other fa.tors such a. produce ma.urity, ripening, ha.vest time(during the da. or sea.on) a.d time la.se a.ter ha.vest. The susceptibility to bruising is pa.tly dependent on how these fa.tors a.ter the produce physiologica. a.d biochemica. properties, a.d the environmenta. conditions such a. tempera.ure, humidity a.d severa. other postha.vest trea.ments. Hence, the successful a.plica.ions of ha.vesting techniques by use of tra.ned personnel a.d proper ha.vesting equipment a.e essentia. to reduce both the incidence a.d severity of ***, the ca.eful selection of postha.vest ha.dling tempera.ure a.d other trea.ments ca. increa.e resista.ce of fresh produce to bruise da.a.e.

关键词： bruise da.a.e ha.vest postha.vest fruit qua.ity

来源：

维普期刊数据库

同方期刊数据库评论

在线全文

学校读者我要写书评

暂无评论

Effect of Medium a.idity a.d Photosta.ility of 3-（4-Dimethyl- a.ino-phenyl）-l-（2,5-dimethyl-thiophen-3-yl）-propenone （DDTP）： a.New Green Emitting La.er Dye

引用

Chinese Journa. of Chemistry 2011年第11期29卷 2557-2561页

作者： EI-Da.y, Sa.y a.a.iri, ab.ullah M. Kha., Sa.ma. a. a.a.ry, Kha.id a. hussein, Ma.moud a. Chemistry Depa.tment Faculty of Science King Abdulaziz University P.O. Box 80203 Jeddah 21589 Saudi Arabia Depa.tment of Chemistry Faculty of Science Tanta University 31527 Tanta Egypt The Center of Excellencefora.va.ced Ma.eria.s King Abdul Aziz University Jeddah 21589 P.O. Box 80203 Saudi Arabia Polymer Chemistry La. Chemistry Department Faculty of Science Assiut University Assiut 71516 Egypt

On the line of a.previous work on the spectra. properties of some of heteroa.yl cha.cone, the effect of medium a.idity a.d photorea.tivity of 3-（4-dimethyla.ino-phenyl）-l-（2,5-dimethyl-thiophen-3-yl）-propenone （DDTP） ha. been investiga.ed in dimethylforma.ide a.d in chlorometha.e solvents such a. methylenechloride, chloroform a.d ca.bon tetra.hloride. The dye solution （ca. 5×10^-4 mol·L^-1 in DMF） gives a.good la.er emission in the ra.ge 470 --560 nm with emission ma.imum a. 515 nm upon pumping by nitrogen la.er （λex=337.1 nm）. The la.er pa.a.eters such a. ga.n coefficient （a., emission cross section （Cre） a.d ha.f life energy （E1/2） a. ma.imum la.er emission a.e a.so determined.

关键词： 3-(4-dimethyla.ino-phenyl)-1-(2,5-dimethyl-thiophen-3-yl)-propenone la.er dyes effect of a.idity possibility

来源：

维普期刊数据库评论

在线全文

维普期刊数据库

学校读者我要写书评

暂无评论

欢迎您,

建议与咨询留下您的常用邮箱和电话号码，以便我们向您反馈解决方案和替代方法

时间限定

文献类型

馆藏选择

核心期刊

语言

文献类型

帮助

文字说明：

检索规则说明：

检索范例：

分类表

所选分类

限定检索结果

文献类型

馆藏范围

日期分布

学科分类号

主题

机构

作者

语言

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

请选择保存的检索档案：

请选择收藏分类：

通借通还

欢迎您,

建议与咨询 留下您的常用邮箱和电话号码，以便我们向您反馈解决方案和替代方法

时间限定

文献类型

馆藏选择

核心期刊

语言

文献类型

帮助

文字说明：

检索规则说明：

检索范例：

分类表

所选分类

限定检索结果

文献类型

馆藏范围

日期分布

学科分类号

主题

机构

作者

语言

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

在线全文

请选择保存的检索档案： 新增检索档案 确定 取消

请选择收藏分类： 新增自定义分类 确定 取消

通借通还

建议与咨询留下您的常用邮箱和电话号码，以便我们向您反馈解决方案和替代方法

请选择保存的检索档案：

请选择收藏分类：