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Alobar Holoprosencephaly in a Neonate: A Rare Case Report and Review of the Literature

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Open Journal of Pediatrics 2023年第6期13卷 929-933页

作者： hanae bahari Hanane Hajaj Anass Ayyad Sahar Messaoudi Rim Amrani Department of Neonatology Intensive Care Unit University Mohammed First Oujda Morocco The Maternal-Child & Mental Health Research Laboratory Oujda Morocco

Holoprosencephaly (HPE) is a rare brain malformation with multiple etiologies and is often associated with suggestive facial anomalies. This pathology is the result of a defect in the early development of the forebrain. There are three clinical forms: lobar, semi-lobar, alobar and another milder subtype of HPE called middle interhemispheric. In this clinical case, we present a newborn with alobar holoprosencephaly and we highlight the clinical, radiological and progressive clinical aspects of this illness during the neonatal period.

关键词： Polymalformative Syndrome Holoprosencephaly Hydrocephalus

Pediatric Hepatoblastoma: A Case Report and Review of the Literature

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Open Journal of Pediatrics 2024年第2期14卷 266-271页

作者： hanae bahari Hanane Hajaj Hind Zahiri Ayyad Ghanam Abdeladim Babakhouya Maria Rkain Department of Pediatrics Mohammed VI University Hospital Oujda Morocco Medical School Mohammed First University Oujda Morocco

Introduction and Objective: Hepatoblastoma is the most frequent malignant embryonal liver tumor, and its incidence is increasing. Children under 3 years of age are particularly affected. The etiology is largely unknown, but a genetic predisposition exists. This case highlights the clinical and imaging characteristics and management strategies. Case Report: We report the case of an 18 months old male admitted for exploration of an abdominal mass and was diagnosed with hepatoblastoma. Conclusion: Hepatoblastoma is an aggressive tumor that begins locally and eventually metastasizes to the brain, lungs, lymph nodes, and other organs. Tumor stage at presentation and resectability are the most significant prognostic factors.

关键词： Hepatoblastoma Liver Children Alpha-Fetoprotein

Macrophage Activation Syndrome as the Primary Presentation of Pediatric Systemic Lupus Erythematosus: A Case Report and Review of the Literature

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Open Journal of Pediatrics 2024年第1期14卷 132-138页

作者： Hanane Hajaj hanae bahari Aziza El Ouali Ayyad Ghanam Maria Rkain Abdeladim Babakhouya Department of Pediatrics Mohammed VI University Hospital Oujda Morocco Mohammed VI University Hospital Medical School University Mohammed First Oujda Morocco

Macrophage activation syndrome (MAS), in its secondary form, often complicates rheumatic diseases but rarely constitutes a mode of revelation. Systemic lupus erythematosus (SLE) is a systemic autoimmune disease of unknown etiology that primarily affects women in adulthood. MAS is a serious condition that may be the first presentation of SLE. Here, we report the case of a 4-year-old female with MAS as the primary manifestation of Systemic Lupus Erythematosus (SLE). In this case, we outline the characteristics of a complex case of SLE that was initially accompanied with MAS, and also review the literature to discuss the clinical, biological, and therapeutic aspects of this condition.

关键词： Macrophage Activation Syndrome Systemic Lupus Erythematosus Child

Extra Dural Hematoma of the Dorso-Lumbar Region in a Hemophiliac: A Rare Entity

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Open Journal of Pediatrics 2024年第1期14卷 84-88页

作者： Hanane Hajaj hanae bahari Ayyad Ghanam Aziza El Ouali Abdeladim Babakhouya Maria Rkain Department of Pediatrics Mohammed VI University Hospital Oujda Morocco Faculty of Medicine and Pharmacy Mohammed Ist University Oujda Morocco

Introduction and objective: Hemophilia is a genetic bleeding disorder inherited as a recessive train linked to the male gender. Bleeding into the central nervous system in patients with hemophilia is an extremely dangerous condition that can be directly life-threatening, if left untreated. Extradural hematoma of the dorso-lumbar region is rare but potentially deadly disease in children. This condition can result in severe neurological deficits. We aim to discuss the clinical, radiological and progressive clinical aspects of this illness. Case report: We report the case of a 5-year-old child with severe hemophilia A treated for extradural hematoma of the dorso-lumbar region resulting from trauma. A spinal magnetic resonance imaging revealed an extradural hematoma. The patient was successfully treated with intensive replacement therapy and did not require surgical intervention. Conclusion: Extradural hematoma is a rare complication of hemophilia, that needs to be looked for in children who have bleeding disorders. For the best neurological outcome, early diagnosis is crucial.

关键词： Extradural Hematoma Children Hemophilia

Sacrococcygeal Teratoma a Rare Tumor in Children: Case Report

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Open Journal of Pediatrics 2024年第1期14卷 78-83页

作者： hanae bahari Hanane Hajaj Hind Zahiri Ayyad Ghanam Aziza El Ouali Abdeladim Babakhouya Maria Rkain Department of Pediatrics Mohammed VI University Hospital Oujda Morocco Medical School University Mohammed First Oujda Morocco

Sacrococcygeal teratomas (SCTs) are uncommon congenital tumors that typically develop in newborns, they are rarely associated with chromosomal abnormalities or other congenital anomalies. The majority of pediatric teratomas are benign in the neonatal age group, but the risk of malignancy increases with age. Diagnosis is based on a combination of clinical, radiological, and hormonal findings, but confirmed by anatomopathological study. Treatment is primarily surgical, with the aim of achieving complete resection to prevent recurrence. We present the case of a 22-month-old child who was admitted for management of a sacrococcygeal mass and was diagnosed with an immature teratoma.

关键词： Sacrococcygeal Mass Alpha-Fetoprotein Surgery

Ecthyma Gangrenosum in Patient with Bone Marrow Aplasia: A Case Report and Review of the Literature

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Open Journal of Pediatrics 2024年第2期14卷 272-278页

作者： Hanane Hajaj hanae bahari Hind Zahiri Ayyad Ghanam Aziza El Ouali Abdeladim Babakhouya Maria Rkain Department of Pediatrics Mohammed VI University Hospital Oujda Morocco Mohammed VI University Hospital Medical School Mohammed First University Oujda Morocco

Background: Ecthyma gangrenosum (EG) is an infrequent and discernible cutaneous disease caused by Pseudomonas aeruginosa. In situations where it is associated with septicemia in debilitated patients, the prognosis is usually unfavorable. Objective: In this case, we aim to verify risk factors, clinical, bacteriological and therapeutic characteristics of ecthyma gangrenosum and we review the literature to highlight the features of this rare condition and discuss the role of early diagnosis and treatment. Case Report: We describe the clinical case of a 4-year-old male with bone marrow aplasia who was presented with characteristic skin lesions of EG and developed sepsis later. Conclusion: EG is a cutaneous disease characterized by its aggressive nature. The presence of delayed diagnosis and therapy, along with sepsis, is closely linked to a high mortality rate. Treatment is empirically founded on an aggressive initial approach.

关键词： Ecthyma Gangrenosum Child Bone Marrow Aplasia