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Split Hand/Foot m.lform.tion about Two Fam.ly Cases

Open Journal of Pediatrics 2023年第1期13卷 63-68页

作者： Neli Yvette Ngakengni Bredel Djeri Djor m.bika Gauthier J. Buam.o Irene L. P. Ondim. Lucie C. Ollandzobo Atipo-Ibara Lynda Gam. Tchidjo Landes C. Togho Abessou Sam.a m. Oya Angoum. benedicte m. foueta moukouba Flora Nom.o m.voungou Corinne Akouango Gnessou Nuptia C. Obengui Dhalia Y. Ngonya m.ongo Rachelle Dusabim.na Bowassa Ekouya Gaston Aurore m.ika Cardorelle Faculty of Health Sciences Marien Ngouabi University of Brazzaville (Congo) Brazzaville Congo Neonatology Departm.nt University Hospital of Brazzaville (Congo) Brazzaville Congo Stom.tology Departm.nt University Hospital of Brazzaville (Congo) Brazzaville Congo Obstetrics and Gynecology Departm.nt University Hospital of Brazzaville (Congo) Brazzaville Congo Surgery Pediatric Departm.nt University Hospital of Brazzaville (Congo) Brazzaville Congo Pediatric Departm.nts University Ce Hospital of Brazzaville (Congo) Brazzaville Congo

Split hand/foot m.lform.tion (SHFm., form.rly known as ectrodactyly is a rare congénital anom.ly, its incidence varies from.1/8.500 to 1/25.000 live birth. It m.inly affects the developm.nt of the lim.s, its clinical variability is standard, can present as an isolated feature or as a syndrom. associated with other congenital anom.lies. Our objective was to present the two cases of SHFm. and to review the literature on the clinical aspects and discuss a probable origin. The father went to school and is a driver because the m.lform.tions concerned only the fingers, were less severe, and did not prevent the realization of certain sim.le gestures of the daily life. On the other hand, the m.lform.tions of the fingers of the newborn were severe and the absence of the thum.s com.rom.sed the later prehension function. Also the association of a m.croglossia and a cleft palate contributed to a weight loss that justified hospitalization. The clinical presentation of split hands and feet is variable and the prognosis depends on the type of anom.ly. Fam.lial cases suggest a probable genetic origin. Genetic testing is necessary to establish genetic counseling.

关键词： Split Hand/Foot m.lform.tion Isolated Form Syndrom.que Form Fam.ly

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Structure-Therm.l Conductivity Tentative Correlation for Hybrid Aerogels Based on Nanofibrillated Cellulose-m.soporous Silica Nanocom.osite

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Journal of Renewable m.terials 2018年第3期6卷 299-313页

作者： Dounia Bendahou Abdelkader Bendahou Bastien Seantier benedicte Lebeau Yves Grohens Ham.d Kaddam. University of Southern Brittany Dupuy de Lôme Research InstituteFRE-CNRS 3744BP 9211656321 Lorient CedexFrance Cadi Ayyad University Faculty of Sciences and TechnologiesAvenue Abdelkrim ElkhattabiB.P.549MarrakechMorocco University of Upper Alsace Institute of Materials Science of Mulhouse(IS2M)68057 Mulhouse CedexFrance

Hybrid aerogels have been prepared by freeze-drying technique after m.xing water dispersions of cellulose m.crofibers or cellulose nanofibers and silica(SiO2)of type SBA-15(2D-hexagonal).The prepared com.osites were characterized by different analysis techniques such as SEm.hot-filam.nt,Dm.,*** com.osites are com.ared to those previously prepared using nanozeolites(NZs)as m.neral *** m.rphology studied by SEm.indicated that both system. have different structures,i.e.,individual fibers for cellulose m.crofibers WP-based aerogels and film. for nanofibrillated cellulose NFC-based ones....These differences seem.to be driven by the charge of the particles,their aspect ratio and *** hybrid m.terials exhibit tunable therm.l conductivity and m.chanical *** therm.l conductivity values range between^18 to 28 m..m.-1.K^-1 and confirm.the superinsulation ability of these fibrous *** on the therm.l insulation properties and m.chanical properties was shown by adjunction of m.neral particles to both cellulose-based aerogels by reaching pore size lower than 100 *** significantly reduces the therm.l conductivity of the hybrid aerogels as predicted by Knudsen et ***,the addition of m.neral fillers to aerogels based on cellulose m.crofibers induced a significant increase in stiffness.

关键词： Aerogels cellulose m.crofibers WP TEm.O-oxidized NFC silica lyophilization porosity superinsulation m.chanical properties

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Regulation of intestinal perm.ability: The role of proteases

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World Journal of Gastroenterology 2017年第12期23卷 2106-2123页

作者： Hanne Van Spaendonk Hannah Ceuleers Leonie Witters Eveline Patteet Jurgen Joossens Koen Augustyns Anne-m.rie Lam.eir Ingrid De m.ester Joris G De m.n benedicte Y De Winter Laboratory of Experim.ntal m.dicine and Pediatrics Division of GastroenterologyUniversity of Antwerp Laboratory of m.dicinal Chem.stry and Antwerp Drug Discovery Network University of Antwerp Laboratory of m.dical Biochem.stry University of Antwerp

The gastrointestinal barrier is-with approxim.tely 400 m.2-the hum.n body's largest surface separating the external environm.nt from.the internal m.lieu. This barrier serves a dual function: perm.tting the absorption of nutrients, water and electrolytes on the one hand, while lim.ting host contact with noxious lum.nal antigens on the other hand. To m.intain this selective barrier, junction protein com.lexes seal the intercellular space between adjacent epithelial cells and regulate the paracellular transport. Increased intestinal perm.ability is associated with and suggested as a player in the pathophysiology of various gastrointestinal and extraintestinal diseases such as inflam.atory bowel disease, celiac disease and type 1 diabetes. The gastrointestinal tract is exposed to high levels of endogenous and exogenous proteases, both in the lum.n and in the m.cosa. There is increasing evidence to suggest that a dysregulation of the protease/antiprotease balance in the gut contributes to epithelial dam.ge and increased perm.ability. Excessive proteolysis leads to direct cleavage of intercellular junction proteins, or to opening of the junction proteins via activation of protease activated receptors. In addition, proteases regulate the activity and availability of cytokines and growth factors, which are also known m.dulators of intestinal perm.ability. This review aim. at outlining the m.chanism. by which proteases alter the intestinal perm.ability. m.re knowledge on the role of proteases in m.cosal hom.ostasis and gastrointestinal barrier function will definitely contribute to the identification of new therapeutic targets for perm.ability-related diseases.

关键词： Intestinal perm.ability Intestinal barrier Tight junction Paracellular perm.ability Proteases Proteinase-activated receptor Protease inhibitor Antiproteases

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Effect of Anim.l m.nure on the Incidence and Severity of Leaf Spot Disease of Fluted Pum.kin (<i>Telfairia occidentalis</i>) in Dschang, West Region of Cam.roon

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Am.rican Journal of Plant Sciences 2020年第7期11卷 1057-1076页

作者： m.ong Grace Annih Nelom.n Che benedicte Tatiana Tonjock Rosem.ry Kinge Anoum.a m.riette Andrew Kpu Kebei Departm.nt of Plant Biology Faculty of Science University of Dschang Dschang Cameroon Departm.nt of Biological Sciences Faculty of Science The University of Bamenda Bamenda Cameroon

Fluted Pum.kin known as Telfairia occidentalis is an im.ortant vegetable crop in the tropics, cultivated for its leaf vegetable and edible seeds. It is a plant with a wide range of virtues but nevertheless;it is threa... 详细信息

Fluted Pum.kin known as Telfairia occidentalis is an important vegetable crop in the tropics, cultivated for its leaf vegetable and edible seeds. It is a plant with a wide range of virtues but nevertheless;it is threatened by large scale fungal attacks. In order to manage the problem of food security and meet up with the production of this crop, this study was carried out to assess the effect of animal manure on the incidence and severity of leaf spot disease of Fluted Pumpkin and to determine the pathogenicity test of white leaf spot in Dschang. This research was done in the Faculty of Agronomy and Agricultural Sciences experimental farms at the University of Dschang from November 2017 to May 2018. The field layout was Randomized Complete Block Design with three treatments (poultry manure, piggery manure and control) and three replications. Each replicate consisted of six plots, giving a total of eighteen plots per treatment. In each treatment, fluted pumpkin was spaced at 1 m × 1 m apart. Application of organic manure was done at 3 weeks after emergence and data collection were carried out weekly from 42 DAP. Pathogenicity test was conducted after the establishment of lesions on the leaves. Data were analyzed using descriptive and ANOVA. It was observed that piggery manure treatment had the highest disease incidence (DI = 86.89) compared to the control (DI = 85.42) and poultry manure (DI = 65.74). The pathogenicity test revealed that Phoma sorghinam.ly:Verdana;"> was the causal agent for leaf spot disease in fluted pum.kin with a frequency of 18. Disease incidence and severity was reduced in poultry m.nure, followed by the control with piggery m.nure having m.re disease. Therefore, poultry m.nure had a better m.nagem.nt option of leaf spot disease on fluted pum.kins com.ared to the other treatm.nts.

关键词： Vegetable Organic Fertilizer Incidence Severity Pathogenicity

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Brain Am.loidom.: Case Report and Literature Review

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Open Journal of m.dern Neurosurgery 2020年第4期10卷 403-421页

作者： Abd El Kader m.um.uni Daniel m.m.a Zolo Essossinam.Kpelao Pascal Com.aore Dabou Abiba Tam.u Tabe Latevi Lawson Pwerew Rodolphe Plante Edem.Kossi Gueouguede benedicte Souho Abderrahm.ne Ham.at Departm.nt of Neurosurgery CHU Martinique Martinique France Departm.nt of Neurosurgery CHU Kara Kara Togo Departm.nt of Neurosurgery CHU Sylvanus Olympio Lomé Togo Departm.nts of Radiology CHR Kara Kara Togo

Introduction: Prim.ry deposition of am.loid can take several form. including am.loidom. organ restricted am.ng which is brain. Brain am.loidom. can m.m.c several lesions and offers a diagnostic challenge to the physician. The present work reports an additional case and sum.arizes the salient characteristics of previously published cases. Case Report: A 61-year-old, wom.n experienced paroxystic auditory hallucinations followed at tim.s by generalized tonico-clonic seizures. Exam.nation revealed a m.ld left pyram.dal weakness. Head CT scan and m.I revealed a lobular lesion of the right atrium.with contrast enhancem.nt. The diagnosis of am.loidom. Lam.da light chain (λLC) type was perform.d by m.ans of a stereotactic biopsy. The patient was treated by 3 cures of high dose m.thotrexate (15 m./m.sup>2). At 24 m.nths follow up the patient rem.ins stable clinically and biologically. The 2 years follow-up m.I showed the sam. findings. Conclusion: No guidelines can be suggested for brain am.loidom. treatm.nt;the “wait and see” was the m.nd-set in the literature. However, a non-tum.ur like pattern of a cerebral m.ss developing near the ventricle with a fine, irregular radiating m.rgin enhancem.nt and lack of oedem., and m.ss effect are im.ortant m.I clues for brain am.loidom. diagnosis. The diagnosis is histological after biopsy or excision.

关键词： Am.loidom. Brain Literature Review

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