Klippel-Trenaunay syndrome with gastrointestinal bleeding,splenic hemangiomas and left inferior vena cava

作     者：Wang, Zhen-Kai Wang, Fang-Yu Zhu, Ren-Min Liu, Jiong 

作者机构：Nanjing Mil Command Chinese PLA Nanjing Cent Hosp Dept Gastroenterol Nanjing 210002 Jiangsu Prov Peoples R China 

出 版 物：《World Journal of Gastroenterology》 (世界胃肠病学杂志（英文版）)

年 卷 期：2010年第16卷第12期

页      面：1548-1552页

核心收录：

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：Klippel-Trenaunay syndrome Gastrointestinal bleeding Splenic hemangiomas Left inferior vena cava 

摘      要：Klippel-Trenaunay syndrome is a congenital vascular anomaly characterized by a triad of varicose veins,cutaneous capillary malformation,and hypertrophy of bone and(or)soft *** vascular malformations in Klippel-Trenaunay syndrome may present with gastrointestinal *** majority of patients with spleenic hemangiomatosis and/or left inferior vena cava are *** herein report a case admitted to the gastroenterology clinic with life-threatening hematochezia and symptomatic iron deficiency *** to the asymptomatic mild intermittent hematochezia,splenic hemangiomas and left inferior vena cava,the patient did not seek any help for gastrointestinal bleeding until his admittance to our department for evaluation of massive gastrointestinal *** was referred to angiography because of his serious pathogenetic condition and inefficiency of medical *** method showed that hemostasis was successfully achieved in the hemorrhage site by embolism of corresponding *** endoscopy revealed vascular malformations starting from the stomach to the descending *** the other hand,computed tomography revealed splenic hemangiomas and left inferior vena *** the best of our knowledge,this is the first Klippel-Trenaunay syndrome case presenting with gastrointestinal bleeding,splenic hemangiomas and left inferior vena *** literature on the evaluation and management of this case is reviewed.