Caroli Disease: A Case Report Observed at the Cocody Teaching Hospital of Abidjan (Cote D’Ivoire)

作     者：A. Ouattara S. Koné E. Allah-Kouadio D. Soro A. W. Ndjitoyap E. Kouadio K. A. Kanga C. D. Fanou M. J. Lohoues-Kouacou B. M. Camara 

作者机构：Service D’Hépato-Gastro Entérologie CHU Cocody Abidjan Côte D’Ivoire Service De Pédiatrie Médicale CHU Cocody Abidjan Côte D’Ivoire Service D’Imagerie Médicale CHU Cocody Abidjan Côte D’Ivoire 

出 版 物：《Open Journal of Gastroenterology》 (肠胃病学期刊（英文）)

年 卷 期：2017年第7卷第1期

页      面：28-31页

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：Carolisyndrom Congenital Cystic Dilation Cholangitis Liver CT-Scan 

摘      要：Caroli disease is a rare affection. It’s commonly associated to polycystic kidneys. We report a case of a nine-year-old girl. She was hospitalized at the pediatric unit of the Cocody Teaching Hospital for an intermittent fever. During the clinical examination, we found a likely cirrhotic hepatomegaly associated to an edematous-ascitic syndrome. Biological exams showed an infectious syndrome with a hyperleukocytosis at 13.000 per mm3, a hyperneutrophilia at 9.600 per mm3. Serological viral markers of B, C and D hepatitis were negative. We saw an intra-hepatic cystic picture at the liver CT-scan with a vascular lesion at his center called a “dot sign. The diagnosis of Caroli disease could be evocated.