Liver fibrosis in primary intestinal lymphangiectasia: An undervalued topic

作     者：Raffaele Licinio Mariabeatrice Principi Enzo Ierardi Alfredo Di Leo 

作者机构：Gastroenterology UnitDepartment of Emergency and Organ TransplantationUniversity of Bari 

出 版 物：《World Journal of Hepatology》 (世界肝病学杂志（英文版）（电子版）)

年 卷 期：2014年第6卷第9期

页      面：685-687页

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：Hepatic transient elastography Liver fibrosis Low-fat diet Primary intestinal lymphangiectasia 

摘      要：The relationship between primary intestinal lymphangiectasia(PIL) and liver fibrosis is an emerging topic with many obscure aspects due to the rarity of the disorder.A recent paper reported that a six-month lowfat diet improved liver *** report the case of a 17-year-old girl affected by PIL whose hepatic fibrosis progressively worsened within one year,despite dietetic *** and the previous case report describe extraordinary events,which do not allow clear-cut clinical aspects to be ***,both cases suggest that in patients with PIL,it is necessary to closely monitor liver morphology with in-depth investigations including not only ultrasonography,but also elastography.