Stenosis of the Subglottic Trachea Revealing Relapsing Polychondritis of a Young Adult

作     者：Mounira El Euch Madiha Mahfoudhi Imen Gorsane Souha Hadded Wifek Bani Moez Karoui Sami Turki Taieb Ben Abdallah 

作者机构：Department of Internal Medicine A Charles Nicolle Hospital Tunis Tunisia 

出 版 物：《International Journal of Clinical Medicine》 (临床医学国际期刊（英文）)

年 卷 期：2015年第6卷第9期

页      面：646-651页

学科分类：1002[医学-临床医学] 100210[医学-外科学(含：普外、骨外、泌尿外、胸心外、神外、整形、烧伤、野战外)] 10[医学] 

主　　题：Relapsing Polychondritis Airway Narrowing Prognosis 

摘      要：Relapsing polychondritis is a rare inflammatory disease involving essentially cartilaginous structures. Other systemic manifestations can be encountered as the eye and ear disturbance. Aortic aneurysms affect few cases. If affection of airway cartilages occurs, prognosis may be worsened by eventual stenotic lesions. We report a 22-year-old woman with Relapsing polychondritis. When she was referred to our hospital 4 weeks after the onset of respiratory symptoms, she was having severe breathing difficulty. Immediate tracheostomy followed by steroid therapy improved her respiratory condition, although the treatment was complicated because of her diabetes. While airway involvement of Relapsing polychondritis can be life threatening, it is curable with steroid therapy. Clinicians should keep in mind that airway obstruction could be caused by this disease.