Retroperitoneal desmoplastic small round cell tumor:Pediatric patient treated with multimodal therapy

作     者：Yong Seok Kim Seong Jae Cha Yoo Shin Choi Beom Gyu Kim Sung Jun Park In Taik Chang 

作者机构：Department of SurgeryCollege of MedicineChung-Ang University 

出 版 物：《World Journal of Gastroenterology》 (世界胃肠病学杂志（英文版）)

年 卷 期：2009年第15卷第33期

页      面：4212-4214页

核心收录：

学科分类：1002[医学-临床医学] 100214[医学-肿瘤学] 10[医学] 

主　　题：Retroperitoneum Desmoplastic small round cell tumor Multimodal therapy 

摘      要：A desmoplastic small round cell tumor (DSRCT) is a rare, aggressive mesenchymal neoplasm. Although a DSRCT can develop at various sites, the intraabdominal site is the most common location. These tumors are found most commonly among young adolescents and the prognosis is extremely poor. Multimodal treatment with surgery, chemotherapy and radiotherapy is very important for these rare cases, and this treatment can improve patient survival. In this report, we describe the case of an 8-year-old boy diagnosed with DSRCT located in the retroperitoneal space. The patient has undergone surgical resection and adjuvant chemoradiation therapy, and is currently alive without disease recurrence.