A Case of mild idiopathic adulthood ductopenia and brief review of literature

作     者：Aung Kaung Vinay Sundaram Deepti Dhall Tram T.Tran 

作者机构：Department of MedicineCedars-Sinai Medical CenterLos AngelesCAUSA Center for Liver Disease and TransplantationCedars-Sinai Medical CenterLos AngelesCAUSA Department of PathologyCedars-Sinai Medical CenterLos AngelesCAUSA 

出 版 物：《Gastroenterology Report》 (胃肠病学报道（英文）)

年 卷 期：2015年第3卷第2期

页      面：167-169页

核心收录：

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：idiopathic adulthood ductopenia idiopathic cholestasis primary biliary cirrhosis small-duct primary sclerosing cholangitis 

摘      要：Mild idiopathic adulthood ductopenia(IAD)is a rare cholestatic disease of unknown cause and characterized by interlobular bile duct loss in less than 50%of the portal *** describe the case of a middLe-aged male who presented with persistent elevation of transaminases and alkaline *** had a normal biliary tree on endoscopic retrograde cholangiopathy and negative anti-mitochondrial *** liver biopsy specimen showed chronic biliary disease,duct loss in 4 out of 15 portal tracts and prominent *** on the work-up,he likely had mild *** transplantation would be necessary if his disease becomes progressive.