Agenesis of the dorsal pancreas

作     者：Wolfgang J Schnedl Claudia Piswanger-Soelkner Sandra J Wallner Robert Krause Rainer W Lipp 

作者机构：Practice for General Internal MedicineHauptstrasse 5A-8940 LiezenAustria Department of Internal MedicineMedical UniversityAuenbruggerplatz 15A-8036 GrazAustria Institute of PathophysiologyCenter for Molecular MedicineHeinrichstrasse 31aA-8010 GrazAustria 

出 版 物：《World Journal of Gastroenterology》 (世界胃肠病学杂志（英文版）)

年 卷 期：2009年第15卷第3期

页      面：376-377页

核心收录：

学科分类：1002[医学-临床医学] 100210[医学-外科学(含：普外、骨外、泌尿外、胸心外、神外、整形、烧伤、野战外)] 10[医学] 

基　　金：Author contributions: Schnedl WJ  Lipp RW gave the conception and designed the letter Sebnedl WJ  Piswanger-Soelkner C analyzed and interpreted the data Schnedl WJ drafted and critically revised the article for important intellectual content Schnedl W J  Wallner S J  Lipp RW finally approved the article Schnedl WJ  Piswanger-Soelkner C  Wallner S J  Krause R  Lipp RW gave the administrative  technical  or logistic support Wallner S J  Krause R  Lipp RW collected and assembled the data 

主　　题：Agenesis of dorsal pancreas Diabetesmellitus Glucose intolerance Abdominal pain Pancreatitis 

摘      要：During the last 100 years in medical literature,there are only 54 reports,including the report of Pasaoglu et al(World J Gastroenterol 2008;14:2915-2916),with clinical descriptions of agenesis of the dorsal pancreas in *** of the dorsal pancreas,a rare congenital pancreatic malformation,is associated with some other medical conditions such as hyperglycemia,abdominal pain,pancreatitis and a few other *** approximately 50% of reported patients with this congenital malformation,hyperglycemia was *** of hyperglycemia and diabetes mellitus in all patients with agenesis of the dorsal pancreas including description of fasting blood glucose,oral glucose tolerance test,glycated hemoglobin and medical treatment would be a future *** autosomal dominant transmission has been suggested in single families,more family studies including imaging technologies with demonstration of the pancreatic duct system are needed for evaluation of this *** this letter to the editor,we aim to increase available information for the better understanding of this rare disease.