An unusual case of Carney triad with high level catecholamine- secreting but no existence of extra-adrenal paraganglioma

作     者：QIAO Gui-bin FANG Yi ZENG Wei-sheng PENG Li-jun HUANG Wen-jie 

作者机构：Department of Thoracic Surgery General Hospital of Guangzhou Military Command of Chinese People's Liberation Army Guangzhou Guangdong 510010 China Department of Respiratory Medicine General Hospital of Guangzhou Military Command of Chinese People's Liberation Army Guangzhou Guangdong 510010 China 

出 版 物：《Chinese Medical Journal》 (中华医学杂志（英文版）)

年 卷 期：2010年第123卷第4期

页      面：510-512页

核心收录：

学科分类：0710[理学-生物学] 090601[农学-基础兽医学] 1002[医学-临床医学] 07[理学] 09[农学] 0906[农学-兽医学] 071006[理学-神经生物学] 

主　　题：Carney triad pulmonary chondroma gastrointestinal stromal tumor paraganglioma 

摘      要：In 1977, Carney originally described the association of .gastric epithelioid leiomyosarcoma, pulmonary chondroma and extra-adrenal paraganglioma, and this unusual syndrome was subsequently called ＂Carney triad＂. At present, the diagnosis of Carney triad, requires at least two of three components-gastrointestinal stromal tumor （GIST）, pulmonary chondroma and extra-adrenal paraganglioma. Up to now, fewer than 80 cases of Carney triad have been reported worldwide.1 ^We described a case of incomplete Carney triad with multiple pulmonary chondromas and GIST. Although the patient was detected in high level secreting of catecholamine, no extra-adrenal paraganglioma has been found.