Sclerosing epithelioid fibrosarcoma of the pancreas:A case report

作     者：Meng-Qing Sun Li-Na Guo Yan You Yan-Yu Qiu Xiao-Dong He Xian-Lin Han 

作者机构：Department of General SurgeryPeking Union Medical College HospitalChinese Academy of Medical SciencesBeijing 100730China Department of PathologyPeking Union Medical College HospitalChinese Academy of Medical SciencesBeijing 100730China 

出 版 物：《World Journal of Clinical Cases》 (世界临床病例杂志)

年 卷 期：2024年第12卷第26期

页      面：5983-5989页

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 100214[医学-肿瘤学] 10[医学] 

基　　金：Supported by National High Level Hospital Clinical Research Funding,No.2022-PUMCH-B-003 National Multidisciplinary Cooperative Diagnosis and Treatment Capacity Building Project for Major Diseases 

主　　题：Sclerosing epithelioid fibrosarcoma of the pancreas Abdominal malignant fibroblastic soft tissue tumor Abdominal enhanced computed tomography Laparoscopic pancreaticoduodenectomy Case report 

摘      要：BACKGROUND A sclerosing epithelioid fibrosarcoma(SEF)is a rare malignant fibroblastic soft tissue tumor that rarely occurs in intra-abdominal organs.A case of a SEF in the pancreatic head is reported herein,including its clinical manifestations,preoperative imaging features,gross specimen and pathological *** SUMMARY A 33-year-old male patient was admitted to Peking Union Medical College Hospital in December 2023 due to a one-year history of intermittent upper abdominal pain and the discovery of a pancreatic *** patient underwent an enhanced computed tomography scan of the abdomen,which revealed a welldefined,round mass with clear borders and calcifications in the pancreatic *** mass exhibited progressive,uneven mild enhancement,measuring approximately 6.6 cm×6.3 *** patient underwent laparoscopic pylorus-preserving *** pathological examination revealed that the lesion was consistent with a *** the 3-month postoperative follow-up,the patient did not report any short-term complications,and there were no signs of tumor *** SEFs are rare malignant fibrous soft tissue *** rarely develop in the pancreas,and its preoperative diagnosis depends on imaging findings,with confirmation depending on pathological examination and ***,only four cases of pancreatic SEF have been reported in studies written in *** case is the first reported case of a pancreatic SEF by a clinical physician.