Bicuspid aortic valve with associated aortopathy, significant left ventricular hypertrophy or concomitant hypertrophic cardiomyopathy: A diagnostic and therapeutic challenge

作     者：Ivana Sopek Merkaš Nenad Lakušić Mladen Predrijevac KrešimirŠtambuk Maja Hrabak Paar 

作者机构：Department of CardiologySpecial Hospital for Medical Rehabilitation Krapinske TopliceKrapinske Toplice 49217Croatia Department of Clinical MedicineFaculty of Dental Medicine and Health OsijekJ.J.Strossmayer University of OsijekOsijek 31000Croatia Department of Internal MedicineFamily Medicine and History of MedicineFaculty of Medicine OsijekJ.J.Strossmayer University of OsijekOsijek 31000Croatia Department of Cardiovascular SurgeryMagdalena Clinic for Cardiovascular DiseasesKrapinske Toplice 49217Croatia Department of CardiologyMagdalena Clinic for Cardiovascular DiseasesKrapinske Toplice 49217Croatia Department of Diagnostic and Interventional RadiologyUniversity Hospital Centre ZagrebZagreb 10000Croatia School of MedicineUniversity of ZagrebZagreb 10000Croatia 

出 版 物：《World Journal of Clinical Cases》 (世界临床病例杂志)

年 卷 期：2023年第11卷第18期

页      面：4251-4257页

核心收录：

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：Bicuspid aortic valve Left ventricular hypertrophy Left ventricular tract obstruction Hypertrophic cardiomyopathy Aortopathy Multimodal imaging 

摘      要：Due to its prevalence of 0.5%to 2%in the general population,with a 75%predominance among men,bicuspid aortic valve is the most common congenital heart *** is frequently accompanied by other cardiac congenital anomalies,and clinical presentation can vary significantly,with stenosis being the most common manifestation,often resulting in mild to moderate concentric hypertrophy of the left *** is the primary diagnostic modality utilized for establishing the diagnosis,and it is often the sole diagnostic tool relied upon by ***,due to the heterogeneous clinical presentation and possible associated anomalies(which are often overlooked in clinical practice),it is necessary to employ various diagnostic methods and persist in finding the accurate diagnosis if multiple inconsistencies *** employing this approach,we can effectively manage these patients and provide them with appropriate *** a clinical case from our practice,we provide an overview of the literature on bicuspid aortic valve with aortophaty and the possible association with hypertrophic cardiomyopathy,diagnostic methods,and treatment *** review article highlights the critical significance of achieving an accurate diagnosis in patients with bicuspid aortic valve and significant left ventricular *** is crucial to exclude other possible causes of left ventricular outflow tract obstruction,such as sub-or supra-aortic obstructions,and hypertrophic cardiomyopathy.