Current guidelines for diagnosis and management of hepatic involvement in hereditary hemorrhagic teleangiectasia

作     者：Luca Ielasi Matteo Tonnini Fabio Piscaglia Ilaria Serio 

作者机构：Department of Medical and Surgical SciencesUniversity of BolognaBologna 40138Italy Department of Internal MedicineOspedale per gli Infermi di FaenzaFaenza 48018Italy Division of Internal MedicineHepatobiliary and Immunoallergic DiseasesIRCCS Azienda Ospedaliero-Universitaria di BolognaBologna 40138Italy 

出 版 物：《World Journal of Hepatology》 (世界肝病学杂志（英文版）（电子版）)

年 卷 期：2023年第15卷第5期

页      面：675-687页

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：involvement diagnosis hemorrhagic 

摘      要：Hereditary hemorrhagic teleangiectasia(HHT),also known as Rendu-Osler-Weber syndrome,is the most common cause of hepatic vascular malformations in *** vascular shunts(arteriovenous,arterioportal or portovenous)lead to different clinical *** though no hepatic-related symptoms are reported in the majority of cases,the severity of liver disease could lead to refractory medical conditions,in some cases requiring liver *** aim of this manuscript is to provide an updated overview of the current evidence regarding the diagnosis and treatment of HHT liver involvement and liver-related complications.