An Unusual Cause of Irritability in a Single Ventricle Patient after Bidirectional Glenn Shunt

作     者：Sarah Pradhan Eileen Broomall Russel Hirsch 

作者机构：The Heart InstituteCincinnati Children’s Hospital Medical CenterUniversity of Cincinnati College of MedicineCincinnatiOhioUSA Division of NeurologyCincinnati Children’s Hospital Medical CenterDepartment of PediatricsUniversity of Cincinnati College of MedicineCincinnatiOhioUSA 

出 版 物：《Congenital Heart Disease》 (先天性心脏病（英文）)

年 卷 期：2021年第16卷第4期

页      面：393-396页

核心收录：

学科分类：1004[医学-公共卫生与预防医学(可授医学、理学学位)] 1002[医学-临床医学] 1010[医学-医学技术（可授医学、理学学位）] 0703[理学-化学] 100214[医学-肿瘤学] 0702[理学-物理学] 1009[医学-特种医学] 10[医学] 

主　　题：Single ventricle bidirectional Glenn shunt idiopathic intracranial hypertension pseudotumor cerebri 

摘      要：The differential diagnosis for irritability in children is *** patients with congenital heart disease,one must strongly consider cardiac etiologies such as low cardiac output or elevated central venous pressure(CVP).In patients with single-ventricle physiology,the second stage of palliation includes bidirectional Glenn,which involves anastomosis of the superior vena cava to the pulmonary artery resulting in volume offloading of the single systemic ***,early in the post-operative period,patients may experience a headache due to the acute increase in CVP,and symptoms improve over *** intracranial hypertension(IIH),also known as pseudotumor cerebri,is a rare neurologic disorder in children,characterized by raised intracranial pressure(ICP)in the absence of brain parenchymal lesions or cerebrospinal fluid(CSF)*** the pathogenesis of IIH is unknown,early recognition and treatment of IIH are important to prevent permanent vision *** are only rare reports of IIH in patients with Fontan *** our knowledge,we report the first case of IIH in a 2-year-old female after bidirectional Glenn.