Isolated interrupted aortic arch in an adult:A case report

作     者：Shu-Wen Dong Duo-Duo Di Guan-Xun Cheng 

作者机构：Medical Imaging DepartmentPeking University Shenzhen HospitalShenzhen 518000Guangdong ProvinceChina Medical Imaging DepartmentAnhui Medical UniversityHefei 230000Anhui ProvinceChina 

出 版 物：《World Journal of Clinical Cases》 (世界临床病例杂志)

年 卷 期：2021年第9卷第4期

页      面：992-998页

核心收录：

学科分类：1002[医学-临床医学] 100201[医学-内科学(含：心血管病、血液病、呼吸系病、消化系病、内分泌与代谢病、肾病、风湿病、传染病)] 10[医学] 

主　　题：Interrupted aortic arch Diagnostic imaging Multimodal imaging Patent ductus arteriosus Ventricular septal defect Case report 

摘      要：BACKGROUND Interrupted aortic arch(IAA)is a rare congenital heart disease defined by an interruption of the lumen and anatomical continuity between the ascending and descending major *** is usually found within a few hours or days of *** surgery,the chances of survival are *** IAA patients have an effective collateral circulation established,they can survive into ***,IAA in adults is extremely rare,with few reported *** SUMMARY A 27-year-old woman presented with a 6-year history of progressively worsening shortness of breath and chest tightness on *** had cyanotic lips and clubbing of the fingers.A transthoracic echocardiogram revealed an enlarged heart and dilation of the main pulmonary *** was an abnormal 9 mm passage between the descending aorta and pulmonary *** ventricular septal outflow tract had a 14 mm *** ultrasound suggested a patent ductus arteriosus and computed tomographic angiography showed the absence of the aortic *** diagnoses were ventricular septal defect,patent ductus arteriosus,and definite interruption of the aortic *** surgical correction was recommended,the patient declined due to the surgical risks and was treated with medications to reduce pulmonary artery pressure and treat heart *** condition has been stable for 12 mo of *** Although rare,IAA should be considered in adults with refractory hypertension or unexplained congestive heart failure.